KCNH7

potassium voltage-gated channel subfamily H member 7

Summary

Voltage-gated potassium (Kv) channels represent the most complex class of voltage-gated ion channels from both functional and structural standpoints. Their diverse functions include regulating neurotransmitter release, heart rate, insulin secretion, neuronal excitability, epithelial electrolyte transport, smooth muscle contraction, and cell volume. This gene encodes a member of the potassium channel, voltage-gated, subfamily H. This member is a pore-forming (alpha) subunit. There are at least two alternatively spliced transcript variants derived from this gene and encoding distinct isoforms. [provided by RefSeq, Jul 2008]

Known Variants56 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14028862712:163,228,353G/Tuncertain significance
rs1422104152:163,228,443C/Tuncertain significance
rs9409515992:163,228,556G/Auncertain significance
rs7455109692:163,230,026G/Auncertain significance
rs7809625692:163,230,054T/Clikely benign
rs21054023722:163,236,445A/Cuncertain significance
rs1489380642:163,236,451C/Tuncertain significance
rs15738921852:163,236,474G/Cuncertain significance
rs7656378822:163,236,504C/Tuncertain significance
rs20683302:163,237,390C/Gintron variant
rs1415272512:163,241,247C/Glikely benign
rs1834774232:163,241,275G/Tuncertain significance
rs67578502:163,241,287C/Gbenign
rs3752109572:163,241,319C/Tlikely benign
rs13025798892:163,241,348T/Cuncertain significance
rs1438816022:163,250,969C/Tbenign
rs3755885272:163,250,982C/Tuncertain significance
rs177839772:163,250,987G/Abenign
rs3721322702:163,250,995C/Auncertain significance
rs3718874162:163,253,257C/Tuncertain significance
rs7585950452:163,253,264G/Tuncertain significance
rs1397074862:163,253,323A/Tuncertain significance
rs7567130192:163,256,812T/Cuncertain significance
rs10453801462:163,256,894T/Cuncertain significance
rs3718863892:163,256,904A/Tuncertain significance
rs177169422:163,260,691T/Cregulatory region variant
rs24683103222:163,279,976C/Tuncertain significance
rs121047052:163,291,617C/Tintron variant
rs1380922152:163,291,820G/Alikely benign
rs2003597792:163,291,857C/Tuncertain significance
rs7650074942:163,291,906C/Tlikely benign
rs1426974422:163,302,558G/Alikely benign
rs3692434662:163,302,626C/Tuncertain significance
rs24683636042:163,302,633A/Tuncertain significance
rs1400404452:163,302,886G/Auncertain significance
rs782473042:163,302,901C/Tuncertain significance
rs14042271092:163,302,902G/Auncertain significance
rs1997424222:163,360,979G/Tuncertain significance
rs7812159532:163,360,996T/Clikely benign
rs1511393182:163,361,057C/Auncertain significance
rs24685236722:163,361,071A/Guncertain significance
rs15740388422:163,361,073A/Glikely benign
rs3768151982:163,361,155T/Cuncertain significance
rs412686532:163,361,158T/Abenign
rs7466821972:163,374,244G/Alikely benign
rs7807392852:163,374,394T/Alikely benign
rs1489273252:163,374,436G/Abenign
rs7606101952:163,374,449A/Cuncertain significance
rs9517182012:163,374,485G/Tuncertain significance
rs16913809042:163,374,642C/Auncertain significance
rs9009153732:163,393,447T/Cuncertain significance
rs126149552:163,649,480C/A
rs2018326712:163,693,079C/Tuncertain significance
rs24683084282:163,693,121T/Guncertain significance
rs24683143722:163,694,966T/Guncertain significance
rs7605255592:163,694,977T/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.