KLHDC10

kelch domain containing 10

Summary

Enables ubiquitin-like ligase-substrate adaptor activity. Involved in rescue of stalled ribosome and ubiquitin-dependent protein catabolic process via the C-end degron rule pathway. Located in nucleoplasm. Is active in Cul2-RING ubiquitin ligase complex and cytoplasm. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants11 total

rsidPosition (GRCh37)AllelesClassClinVar
rs10370103347:129,710,568G/Cuncertain significance
rs1808417457:129,717,142C/Aintron variant
rs13644714037:129,736,773T/Guncertain significance
rs7474215147:129,736,796C/Tuncertain significance
rs12343026457:129,756,468C/Tuncertain significance
rs1864092417:129,758,849C/Tintron variant
rs25358716917:129,760,628C/Tuncertain significance
rs5597129397:129,760,711C/Tuncertain significance
rs7586807597:129,764,362A/Tuncertain significance
rs8660897447:129,769,348T/Cuncertain significance
rs25358852307:129,770,429G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.