LAIR1

leukocyte associated immunoglobulin like receptor 1

Summary

The protein encoded by this gene is an inhibitory receptor found on peripheral mononuclear cells, including natural killer cells, T cells, and B cells. Inhibitory receptors regulate the immune response to prevent lysis of cells recognized as self. The gene is a member of both the immunoglobulin superfamily and the leukocyte-associated inhibitory receptor family. The gene maps to a region of 19q13.4 called the leukocyte receptor cluster, which contains at least 29 genes encoding leukocyte-expressed receptors of the immunoglobulin superfamily. The encoded protein has been identified as an anchor for tyrosine phosphatase SHP-1, and may induce cell death in myeloid leukemias. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2014]

Known Variants21 total

rsidPosition (GRCh37)AllelesClassClinVar
rs6090824819:54,863,629T/Gcoding sequence variant
rs135016121519:54,866,927T/Cuncertain significance
rs18963930919:54,867,374C/Aupstream gene variant
rs18425347919:54,867,583C/Tuncertain significance
rs75878381619:54,867,853A/Guncertain significance
rs251403731719:54,867,862A/Guncertain significance
rs57010248619:54,868,120C/Tuncertain significance
rs140338586119:54,868,138A/Guncertain significance
rs75690804419:54,868,193G/Tuncertain significance
rs11765512719:54,868,834G/Aupstream gene variant
rs11310597819:54,870,889G/C
rs76339101819:54,872,588C/Guncertain significance
rs7575344119:54,872,599G/Asynonymous variant
rs37149822319:54,872,628G/Auncertain significance
rs77917364919:54,872,763C/Tuncertain significance
rs52766186619:54,872,769G/Tuncertain significance
rs14375395819:54,872,789G/Auncertain significance
rs251417772119:54,875,922T/Cuncertain significance
rs14425935719:54,881,382A/Cupstream gene variant
rs402184319:54,882,068A/Gregulatory region variant
rs75040562019:54,889,353A/G

Gene information from NCBI Gene. Variant classifications from ClinVar.