LAMP3

lysosomal associated membrane protein 3

Summary

This gene encodes lysosome-associated membrane glycoprotein 3, a type 1 integral membrane protein that belongs to a family of lysosome associated membrane proteins which form part of the glycoconjugate coat present on the inside of the lysosomal membrane. It is predominantly expressed in mature dendritic cells and serves as a marker of dendritic cell maturation. The encoded protein localizes primarily to late endosomes/lysosomes and the MHC class II compartment, where it contributes to antigen processing and presentation during adaptive immune responses. The expression of this gene is inducible under hypoxic conditions via hypoxia-inducible factor 1-alpha signaling. In cancer, this gene is frequently overexpressed and is associated with tumor progression, metastasis, therapy resistance, and poor clinical prognosis in multiple malignancies including breast, cervical, and ovarian cancers. [provided by RefSeq, Feb 2026]

Known Variants36 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1132873513:182,841,929C/Auncertain significance
rs9297800833:182,841,952T/Cuncertain significance
rs7638898283:182,853,604C/Tuncertain significance
rs1504327833:182,853,622C/Tuncertain significance
rs7484188173:182,853,646C/Tlikely benign
rs7615471413:182,853,672G/Auncertain significance
rs7541791193:182,858,350C/Tuncertain significance
rs124930503:182,865,073G/T
rs1424395863:182,865,138G/Aintron variant
rs6833953:182,869,818G/T
rs7705606723:182,870,189C/Tuncertain significance
rs1457944653:182,870,211G/Tuncertain significance
rs5451644973:182,870,221C/Tlikely benign
rs1489862183:182,870,237C/Tuncertain significance
rs15768855483:182,870,242G/Tuncertain significance
rs1152815133:182,870,243C/Tuncertain significance
rs1510595673:182,870,248G/Auncertain significance
rs14573848323:182,870,264T/Cuncertain significance
rs5146363:182,870,436G/C
rs1127540783:182,871,482T/Guncertain significance
rs7512995543:182,871,503C/Tuncertain significance
rs12091515793:182,871,583G/Cuncertain significance
rs7743687093:182,871,685C/Tlikely benign
rs7804373583:182,871,742T/Cuncertain significance
rs7552760713:182,871,753G/Tuncertain significance
rs12885339553:182,871,835A/Cuncertain significance
rs7776180573:182,871,838G/Auncertain significance
rs1147744303:182,871,912G/Auncertain significance
rs3690979743:182,871,951T/Clikely benign
rs1382779273:182,871,964C/Tuncertain significance
rs25306887943:182,872,005A/Glikely benign
rs10512722933:182,872,012T/Guncertain significance
rs7600846943:182,872,074A/Guncertain significance
rs3711269833:182,872,168C/Tuncertain significance
rs713142843:182,878,255C/Tintron variant
rs7761971463:182,880,415G/Alikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.