LGMN

legumain

Summary

This gene encodes a cysteine protease that has a strict specificity for hydrolysis of asparaginyl bonds. This enzyme may be involved in the processing of bacterial peptides and endogenous proteins for MHC class II presentation in the lysosomal/endosomal systems. Enzyme activation is triggered by acidic pH and appears to be autocatalytic. Protein expression occurs after monocytes differentiate into dendritic cells. A fully mature, active enzyme is produced following lipopolysaccharide expression in mature dendritic cells. Overexpression of this gene may be associated with the majority of solid tumor types. This gene has a pseudogene on chromosome 13. Several alternatively spliced transcript variants have been described, but the biological validity of only two has been determined. These two variants encode the same isoform. [provided by RefSeq, Jul 2008]

Known Variants39 total

rsidPosition (GRCh37)AllelesClassClinVar
rs18999760814:93,170,693T/Cuncertain significance
rs7729109614:93,170,976A/Gbenign
rs14922740214:93,171,025C/Tuncertain significance
rs14514967414:93,171,033T/Cuncertain significance
rs37030728114:93,172,914C/Tuncertain significance
rs74901512114:93,172,932C/Tuncertain significance
rs74643867414:93,172,970C/Tuncertain significance
rs801355714:93,173,488T/G
rs76765700914:93,176,027C/Tuncertain significance
rs77466740514:93,176,092C/Tuncertain significance
rs76513385214:93,176,108A/Guncertain significance
rs250371516314:93,176,112C/Tuncertain significance
rs76269298014:93,176,118T/Cuncertain significance
rs20031884914:93,176,153G/Auncertain significance
rs77232305714:93,176,160G/Auncertain significance
rs14454582514:93,178,006T/Guncertain significance
rs37605403114:93,178,024C/Tuncertain significance
rs77183450414:93,178,044G/Auncertain significance
rs90880906014:93,178,053A/Guncertain significance
rs7924303714:93,178,058G/Abenign
rs37038347514:93,178,066T/Cuncertain significance
rs14391441614:93,178,279T/Guncertain significance
rs250373694014:93,179,206T/Cuncertain significance
rs78159522014:93,180,172C/Tlikely benign
rs188995882914:93,180,765T/Guncertain significance
rs77998508114:93,182,560T/Cuncertain significance
rs250376026514:93,182,564A/Cuncertain significance
rs76040542114:93,183,733T/Cuncertain significance
rs36901662014:93,183,744G/Alikely benign
rs14348723414:93,183,771T/Cuncertain significance
rs250377022714:93,183,787C/Tuncertain significance
rs76648177114:93,185,096C/Guncertain significance
rs76203846614:93,185,156G/Auncertain significance
rs76094533014:93,185,176T/Cuncertain significance
rs37685641714:93,199,088A/Guncertain significance
rs131140235714:93,199,116C/Auncertain significance
rs18090110914:93,205,974C/Tintron variant
rs104420881214:93,208,122G/C
rs11599769914:93,209,182T/Cintron variant

Gene information from NCBI Gene. Variant classifications from ClinVar.