LGSN

lengsin, lens protein with glutamine synthetase domain

Summary

This gene encodes a protein with similarity to the GS I members of the glutamine synthetase superfamily. The encoded protein is referred to as a pseudo-glutamine synthetase because it has no glutamine synthesis activity and may function as a chaperone protein. This protein is localized to the lens and may be associated with cataract disease. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2009]

Known Variants41 total

rsidPosition (GRCh37)AllelesClassClinVar
rs9777436436:63,989,931T/Cuncertain significance
rs9775771716:63,989,945A/Tuncertain significance
rs7453574826:63,989,979C/Guncertain significance
rs9164387806:63,990,033C/Guncertain significance
rs2014906886:63,990,111G/Cuncertain significance
rs25331674066:63,990,116A/Guncertain significance
rs350395356:63,990,131T/Cbenign
rs7528458476:63,990,191G/Auncertain significance
rs1998835326:63,990,245C/Tuncertain significance
rs25331681826:63,990,273T/Cuncertain significance
rs5740229406:63,990,304C/Guncertain significance
rs1392951156:63,990,359C/Tuncertain significance
rs7554511316:63,990,371G/Auncertain significance
rs3726680106:63,990,443G/Auncertain significance
rs8683974456:63,990,445G/Alikely benign
rs1427400656:63,990,458C/Tuncertain significance
rs2019831826:63,990,545A/Guncertain significance
rs3732035456:63,990,691C/Auncertain significance
rs3679254646:63,990,723C/Tuncertain significance
rs7524439436:63,990,753G/Cuncertain significance
rs7556903416:63,990,758T/Cuncertain significance
rs25331711946:63,990,780A/Tuncertain significance
rs13197373886:63,990,816C/Tuncertain significance
rs7604314326:63,990,824C/Tuncertain significance
rs7635959086:63,990,829A/Cuncertain significance
rs1479598966:63,990,833T/Clikely benign
rs14127959556:63,990,963T/Cuncertain significance
rs15620034516:63,991,000C/Auncertain significance
rs25331726076:63,991,041T/Cuncertain significance
rs7564160146:63,991,098G/Auncertain significance
rs3688180766:63,995,533C/Tuncertain significance
rs1484497656:63,995,542C/Auncertain significance
rs7686554776:64,004,929T/Cuncertain significance
rs93527746:64,014,812A/Cintron variant
rs107380066:64,148,664C/A
rs77425956:64,161,733C/Tintergenic variant
rs1459313326:64,164,854C/A
rs94493126:64,169,534A/G
rs122133646:64,184,964T/Cintergenic variant
rs26222766:64,190,278A/Gcoding sequence variant
rs28000496:64,202,689A/Tintergenic variant

Gene information from NCBI Gene. Variant classifications from ClinVar.