LIFR

LIF receptor subunit alpha

Summary

This gene encodes a protein that belongs to the type I cytokine receptor family. This protein combines with a high-affinity converter subunit, gp130, to form a receptor complex that mediates the action of the leukemia inhibitory factor, a polyfunctional cytokine that is involved in cellular differentiation, proliferation and survival in the adult and the embryo. Mutations in this gene cause Schwartz-Jampel syndrome type 2, a disease belonging to the group of the bent-bone dysplasias. A translocation that involves the promoter of this gene, t(5;8)(p13;q12) with the pleiomorphic adenoma gene 1, is associated with salivary gland pleiomorphic adenoma, a common type of benign epithelial tumor of the salivary gland. Multiple splice variants encoding two different isoforms have been found for this gene. [provided by RefSeq, Jun 2018]

Known Variants914 total

rsidPosition (GRCh37)AllelesClassClinVar
rs5666123405:38,475,133G/Auncertain significance
rs21123282325:38,475,206T/Cuncertain significance
rs7712105955:38,475,214G/Tuncertain significance
rs1414079875:38,475,302A/Gconflicting classifications of pathogenicity
rs21123284875:38,475,311T/Cuncertain significance
rs9637127675:38,475,317C/Guncertain significance
rs1155722835:38,475,381G/Abenign
rs5601828995:38,475,449G/Cuncertain significance
rs12742227705:38,475,471T/Cuncertain significance
rs10462245:38,475,507A/Gbenign
rs730774465:38,475,557G/Cbenign
rs1886823965:38,475,597C/Tuncertain significance
rs8860606045:38,475,711A/Guncertain significance
rs5710646635:38,475,772G/Tuncertain significance
rs8860606055:38,475,901T/Guncertain significance
rs5562407425:38,475,904G/Cuncertain significance
rs8860606065:38,475,929T/Guncertain significance
rs38224255:38,476,027T/Cbenign
rs8860606075:38,476,030A/Guncertain significance
rs1499324785:38,476,063A/Gbenign
rs8860606085:38,476,155C/Tuncertain significance
rs13936356245:38,476,276T/Cuncertain significance
rs77135315:38,476,341T/Cbenign
rs587557635:38,476,472G/Abenign
rs13474659305:38,476,491T/Cuncertain significance
rs8860606095:38,476,513C/Tuncertain significance
rs38224265:38,476,528A/Tbenign
rs1472027395:38,476,572G/Alikely benign
rs10354656165:38,476,590T/Cuncertain significance
rs1833334595:38,476,637A/Tuncertain significance
rs8860606105:38,476,680T/Cuncertain significance
rs7582750905:38,476,693T/Cuncertain significance
rs358532685:38,476,843C/Tbenign
rs13070696965:38,476,856C/Tuncertain significance
rs559171245:38,476,893G/Abenign
rs5558493655:38,476,896T/Cuncertain significance
rs13929939115:38,476,898T/Cuncertain significance
rs2018561415:38,476,962G/Tuncertain significance
rs5761069815:38,477,079A/Guncertain significance
rs8860606135:38,477,259T/Cuncertain significance
rs100566575:38,477,269A/Guncertain significance
rs8860606145:38,477,280T/Cuncertain significance
rs5420943435:38,477,283C/Tuncertain significance
rs1913970585:38,477,292C/Guncertain significance
rs1846424995:38,477,351C/Tuncertain significance
rs8860606155:38,477,433A/Cuncertain significance
rs737492555:38,477,454T/Cbenign
rs730774485:38,477,543T/Clikely benign
rs730774495:38,477,641C/Abenign
rs1405015815:38,477,673C/Tuncertain significance
rs9687852505:38,477,677A/Cuncertain significance
rs12383369555:38,477,845G/Cuncertain significance
rs784742835:38,477,846A/Tlikely benign
rs8860606165:38,477,847A/Cuncertain significance
rs341303185:38,477,863G/Cbenign
rs14329173215:38,477,944C/Guncertain significance
rs1443322225:38,477,949A/Gconflicting classifications of pathogenicity
rs12191098075:38,478,134A/Guncertain significance
rs8864679835:38,478,227C/Auncertain significance
rs1477931035:38,478,248C/Auncertain significance
rs7788882275:38,478,322T/Cuncertain significance
rs1488279945:38,478,367G/Tbenign
rs8681974115:38,478,395A/Guncertain significance
rs7581929475:38,478,515C/Tuncertain significance
rs1424955395:38,478,534A/Guncertain significance
rs17438251255:38,478,535A/Cuncertain significance
rs5524752685:38,478,612C/Auncertain significance
rs21123404335:38,478,623T/Cuncertain significance
rs3681099845:38,478,787C/Tuncertain significance
rs9522928185:38,478,872C/Tuncertain significance
rs12901285525:38,478,951A/Tuncertain significance
rs5476888415:38,478,985G/Alikely benign
rs8860606175:38,479,000T/Cuncertain significance
rs9059266045:38,479,086G/Auncertain significance
rs12840353045:38,479,112A/Tuncertain significance
rs1137307515:38,479,127C/Glikely benign
rs1124580595:38,479,130C/Tlikely benign
rs5558487445:38,479,221C/Auncertain significance
rs1405833275:38,479,233G/Cuncertain significance
rs9252674595:38,479,260T/Cuncertain significance
rs14610848705:38,479,337T/Guncertain significance
rs5514242325:38,479,655T/Cuncertain significance
rs12277419885:38,479,725G/Auncertain significance
rs7594589085:38,479,729T/Guncertain significance
rs5585035905:38,479,745T/Cuncertain significance
rs602870855:38,479,827C/Tbenign
rs7483533975:38,479,837A/Cuncertain significance
rs7722529185:38,479,838T/Guncertain significance
rs8860606185:38,479,842T/Auncertain significance
rs8860606195:38,479,843G/Auncertain significance
rs1902098755:38,479,857G/Cbenign
rs5337373065:38,479,918T/Cuncertain significance
rs10093237225:38,480,054C/Tuncertain significance
rs27319645:38,480,087A/Cbenign
rs14286045:38,480,143G/Cbenign
rs5473198355:38,480,157T/Cuncertain significance
rs753684665:38,480,213T/Cbenign
rs5675651305:38,480,223A/Cconflicting classifications of pathogenicity
rs131565205:38,480,227A/Cbenign
rs8860606205:38,480,229A/Cuncertain significance

Showing 100 of 914 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.