LRR1

leucine rich repeat protein 1

Summary

The protein encoded by this gene contains a leucine-rich repeat (LRR). It specifically interacts with TNFRSF9/4-1BB, a member of the tumor necrosis factor receptor (TNFR) superfamily. Overexpression of this gene suppresses the activation of NF-kappa B induced by TNFRSF9 or TNF receptor-associated factor 2 (TRAF2), which suggests that this protein is a negative regulator of TNFRSF9-mediated signaling cascades. Alternative splicing results in multiple transcript variants.[provided by RefSeq, Feb 2011]

Known Variants28 total

rsidPosition (GRCh37)AllelesClassClinVar
rs76365169614:50,065,776A/Tuncertain significance
rs77307628214:50,065,887C/Guncertain significance
rs1162580414:50,068,299C/T
rs90491103814:50,069,089T/Cuncertain significance
rs76641112314:50,069,148C/Tuncertain significance
rs75557610714:50,069,158A/Guncertain significance
rs75650134914:50,069,161C/Tuncertain significance
rs54692039514:50,069,183T/Guncertain significance
rs250271173614:50,074,190C/Tuncertain significance
rs136089845714:50,074,217A/Tuncertain significance
rs250271207114:50,074,310C/Tuncertain significance
rs250271236114:50,074,409C/Tuncertain significance
rs37600612114:50,074,428A/Cuncertain significance
rs36905172014:50,074,494G/Auncertain significance
rs250271277214:50,074,538A/Cuncertain significance
rs15069097914:50,074,607G/Auncertain significance
rs77141588514:50,074,638T/Cuncertain significance
rs37342715014:50,074,742G/Auncertain significance
rs250271346114:50,074,765A/Tuncertain significance
rs125369910214:50,074,769C/Tuncertain significance
rs20075750414:50,074,826A/Glikely benign
rs2839679814:50,075,319C/G
rs20161483214:50,080,982A/Guncertain significance
rs18622394214:50,080,993A/Guncertain significance
rs20203768214:50,081,029G/Auncertain significance
rs19064743714:50,081,124A/Glikely benign
rs121071464114:50,081,156T/Guncertain significance
rs77884800014:50,081,204T/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.