MBNL2

muscleblind like splicing regulator 2

Summary

This gene is a member of the muscleblind protein family which was initially described in Drosophila melanogaster. This gene encodes a C3H-type zinc finger protein that modulates alternative splicing of pre-mRNAs. Muscleblind proteins bind specifically to expanded dsCUG RNA but not to normal size CUG repeats and may thereby play a role in the pathophysiology of myotonic dystrophy. Several alternatively spliced transcript variants have been described but the full-length natures of only some have been determined. [provided by RefSeq, Mar 2012]

Known Variants14 total

rsidPosition (GRCh37)AllelesClassClinVar
rs477126813:97,865,021T/A
rs7512285913:97,901,005A/Tintron variant
rs78167088913:97,928,608C/Guncertain significance
rs250487997113:97,928,656C/Tuncertain significance
rs197341913:97,976,147T/A
rs76492559613:97,986,614T/Guncertain significance
rs5568400313:97,988,689A/Gintron variant
rs250261278213:97,995,451T/Cuncertain significance
rs250271600413:97,999,149G/Alikely benign
rs102708531113:97,999,307G/Tuncertain significance
rs731825013:98,002,508G/Aintron variant
rs53792913013:98,009,803G/Auncertain significance
rs250297662513:98,009,851G/Alikely benign
rs955671113:98,016,416G/Aupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.