MBOAT1

membrane bound glycerophospholipid O-acyltransferase 1

Summary

This gene belongs to the membrane-bound O-acetyltransferase superfamily. The encoded transmembrane protein is an enzyme that transfers organic compounds, preferably from oleoyl-CoA, to hydroxyl groups of protein targets in membranes. A translocation disrupting this gene may be associated with brachydactyly syndactyly syndrome. Alternately spliced transcript variants have been described for this gene. [provided by RefSeq, Nov 2012]

Known Variants32 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7799038026:20,102,536T/Cuncertain significance
rs24573356:20,109,592G/T
rs11902785506:20,109,832T/Cuncertain significance
rs7498434926:20,109,854C/Tuncertain significance
rs7761351216:20,109,895A/Tuncertain significance
rs2001042206:20,109,905C/Tlikely benign
rs7638827166:20,109,911A/Tuncertain significance
rs1455243766:20,113,119T/Guncertain significance
rs3690534466:20,113,223C/Auncertain significance
rs1435203736:20,113,225C/Auncertain significance
rs7732710786:20,113,226G/Auncertain significance
rs7645690686:20,115,532T/Clikely benign
rs5296800726:20,115,565T/Cuncertain significance
rs7648492796:20,115,573C/Tuncertain significance
rs7523654186:20,115,574T/Cuncertain significance
rs1479811276:20,118,672A/Guncertain significance
rs7458461246:20,118,690T/Cuncertain significance
rs5533533266:20,118,693G/Auncertain significance
rs7663878426:20,124,698C/Guncertain significance
rs7703631476:20,124,729C/Tuncertain significance
rs2009855226:20,124,815T/Cuncertain significance
rs9285074406:20,126,859G/Tuncertain significance
rs7626560256:20,144,492T/Cuncertain significance
rs1490627266:20,151,441T/Auncertain significance
rs1430108056:20,151,450T/Cuncertain significance
rs10412540006:20,151,483G/Auncertain significance
rs7730496926:20,152,879T/Cuncertain significance
rs12188327806:20,152,993A/Guncertain significance
rs12021996:20,156,174T/G
rs109463646:20,177,222T/Aintron variant
rs5550176:20,185,051A/C
rs5762521856:20,214,618G/A

Gene information from NCBI Gene. Variant classifications from ClinVar.