MPO

myeloperoxidase

Summary

Myeloperoxidase (MPO) is a heme protein synthesized during myeloid differentiation that constitutes the major component of neutrophil azurophilic granules. Produced as a single chain precursor, myeloperoxidase is subsequently cleaved into a light and heavy chain. The mature myeloperoxidase is a tetramer composed of 2 light chains and 2 heavy chains. This enzyme produces hypohalous acids central to the microbicidal activity of neutrophils. [provided by RefSeq, Nov 2014]

Known Variants88 total

rsidPosition (GRCh37)AllelesClassClinVar
rs11320325317:56,348,068G/Alikely benign
rs117538943417:56,348,073C/Auncertain significance
rs6174760817:56,348,122G/Abenign
rs130234439617:56,348,130T/Auncertain significance
rs13975274117:56,348,142C/Tuncertain significance
rs3570288817:56,348,208C/Guncertain significance
rs3589705117:56,348,226T/Gsplice region variantpathogenic
rs207140917:56,348,230G/Tbenign
rs20172006417:56,349,050C/Guncertain significance
rs18281492017:56,349,062C/Tuncertain significance
rs76636882917:56,349,073C/Tuncertain significance
rs77439479717:56,349,077C/Auncertain significance
rs54480239517:56,349,095G/Alikely benign
rs36850530817:56,349,111G/Alikely benign
rs11273738217:56,349,122T/Glikely benign
rs14320466417:56,349,128T/Cuncertain significance
rs250913920017:56,349,231G/Tuncertain significance
rs3567008917:56,349,236G/Alikely benign
rs77498420717:56,350,118C/Tuncertain significance
rs197038325717:56,350,121G/Auncertain significance
rs75306206017:56,350,132C/Tuncertain significance
rs75791481217:56,350,163C/Tuncertain significance
rs11946901217:56,350,186A/Cmissense variantpathogenic
rs77347877817:56,350,190G/Alikely pathogenic
rs11946801017:56,350,196G/Amissense variantpathogenic
rs14437123817:56,350,258C/Tuncertain significance
rs14880262517:56,350,259G/Auncertain significance
rs20061856217:56,350,265T/Cuncertain significance
rs155560759917:56,350,773A/Glikely pathogenic
rs117076856017:56,350,861A/Guncertain significance
rs135951278517:56,350,868A/Guncertain significance
rs11946901317:56,350,895C/Tmissense variantpathogenic
rs11946901417:56,350,901G/Amissense variantpathogenic
rs75657285917:56,350,925C/Tuncertain significance
rs77827224817:56,350,926G/Alikely benign
rs6109598717:56,350,986C/Tbenign
rs14913327017:56,351,017C/Tconflicting classifications of pathogenicity
rs2873083517:56,351,019G/Abenign
rs77301165517:56,351,029A/Guncertain significance
rs808213417:56,352,626G/Tintron variant
rs18201121017:56,352,896G/Alikely benign
rs5626121217:56,352,995G/Auncertain significance
rs37155694217:56,353,018G/Tuncertain significance
rs3421210117:56,354,640G/C
rs14890548717:56,355,211G/Alikely benign
rs78041647117:56,355,353C/Tuncertain significance
rs197046068617:56,355,361C/Tuncertain significance
rs2873083717:56,355,397G/Amissense variantpathogenic
rs140251579817:56,355,496T/Cuncertain significance
rs37244663917:56,356,398C/Auncertain significance
rs103144468517:56,356,428C/Tuncertain significance
rs197047668317:56,356,439C/Tuncertain significance
rs37457646317:56,356,440G/Auncertain significance
rs75968460217:56,356,497T/Cuncertain significance
rs5637871617:56,356,502A/Gmissense variantpathogenic
rs75084913817:56,356,523G/Auncertain significance
rs75463289317:56,356,533G/Apathogenic
rs74912018017:56,356,558G/Cuncertain significance
rs147670651117:56,356,568G/Cuncertain significance
rs119261570217:56,356,569C/Tuncertain significance
rs76020136317:56,356,728T/Guncertain significance
rs77801371417:56,356,732C/Aconflicting classifications of pathogenicity
rs77343672917:56,356,765A/Tuncertain significance
rs7895093917:56,356,914T/Cmissense variantpathogenic
rs37224353317:56,356,915A/Guncertain significance
rs14039214517:56,356,937C/Alikely benign
rs57672786517:56,356,974G/Auncertain significance
rs14678268417:56,356,983T/Auncertain significance
rs197049153317:56,357,202G/Auncertain significance
rs18149407717:56,357,221G/Apathogenic
rs197049199517:56,357,222C/Tlikely pathogenic
rs36905264417:56,357,243C/Guncertain significance
rs13826917217:56,357,309C/Tlikely benign
rs77285609017:56,357,310G/Auncertain significance
rs76252688017:56,357,377T/Clikely pathogenic
rs37530097817:56,357,718G/Alikely benign
rs14959023317:56,357,741C/Tlikely benign
rs95796269817:56,357,751T/Cuncertain significance
rs75227756717:56,357,796G/Auncertain significance
rs5592995217:56,357,803C/Tbenign
rs720869317:56,357,818C/Amissense variantbenign
rs285685717:56,357,833G/Aintron variant
rs56056416517:56,358,008C/Auncertain significance
rs155560830217:56,358,010A/Guncertain significance
rs14021598117:56,358,073C/Tlikely benign
rs159804410317:56,358,175G/Anot provided
rs233322717:56,358,762C/Tupstream gene variantrisk factor
rs224382817:56,358,884A/T

Gene information from NCBI Gene. Variant classifications from ClinVar.