MPP4

MAGUK p55 scaffold protein 4

Summary

This gene encodes a member of the membrane-associated guanylate kinase (MAGUK) protein family, with an N-terminal PDZ domain, a central src homology 3 region (SH3), and a C-terminal guanylate kinase-like (GUK) domain. The protein is localized to the outer limiting membrane in the retina, and is thought to function in photoreceptor polarity and the organization of specialized intercellular junctions. Alternatively spliced transcript variants have been described, but their biological validity has not been determined. [provided by RefSeq, Jul 2008]

Known Variants44 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1473739012:202,510,025A/Cuncertain significance
rs3724905442:202,510,081G/Cuncertain significance
rs118941152:202,512,449C/Tuncertain significance
rs7482995782:202,512,461T/Cuncertain significance
rs3740704882:202,512,463C/Tuncertain significance
rs3745179202:202,512,481C/Tuncertain significance
rs2018124682:202,512,504T/Cuncertain significance
rs12882902652:202,512,516C/Guncertain significance
rs3769875702:202,512,532C/Tuncertain significance
rs16876599252:202,514,315A/Guncertain significance
rs7498287922:202,514,397A/Guncertain significance
rs7628540102:202,514,805A/Guncertain significance
rs7455088092:202,519,562G/Auncertain significance
rs7693706152:202,519,570A/Cuncertain significance
rs7718334952:202,519,623C/Guncertain significance
rs2005433942:202,520,956C/Auncertain significance
rs7528612002:202,520,957G/Auncertain significance
rs3681344602:202,520,995A/Guncertain significance
rs13786468832:202,521,037A/Tuncertain significance
rs7630706292:202,521,079C/Tuncertain significance
rs5428049922:202,521,083G/Auncertain significance
rs7637559872:202,525,064G/Cuncertain significance
rs7761877552:202,528,822C/Tuncertain significance
rs16882883422:202,534,464A/Guncertain significance
rs5732318982:202,539,950G/Auncertain significance
rs10575194432:202,539,978A/Gmissense variantpathogenic
rs3746490602:202,545,582G/Cuncertain significance
rs7769791352:202,545,595C/Auncertain significance
rs7648249992:202,545,670C/Tuncertain significance
rs7811853452:202,545,694C/Tuncertain significance
rs1999869512:202,545,700T/Cuncertain significance
rs5581919572:202,545,705G/Cuncertain significance
rs3744075162:202,546,247G/Cuncertain significance
rs3703077802:202,546,280C/Tuncertain significance
rs3740675742:202,546,286A/Guncertain significance
rs7728082832:202,547,592C/Auncertain significance
rs3769644562:202,547,620G/Tuncertain significance
rs1999202242:202,549,852C/Tuncertain significance
rs3727412462:202,549,853G/Auncertain significance
rs1863780212:202,550,699G/Cuncertain significance
rs3677431972:202,552,088C/Tuncertain significance
rs7506317102:202,557,644T/Guncertain significance
rs7793354922:202,557,656G/Auncertain significance
rs5561741892:202,560,577G/C

Gene information from NCBI Gene. Variant classifications from ClinVar.