MRM1

mitochondrial rRNA methyltransferase 1

Summary

Enables rRNA (guanosine-2'-O-)-methyltransferase activity. Involved in rRNA processing. Located in mitochondrial matrix. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants24 total

rsidPosition (GRCh37)AllelesClassClinVar
rs77955450717:34,958,250T/Cuncertain significance
rs20092793817:34,958,256C/Tuncertain significance
rs77234569517:34,958,261C/Tuncertain significance
rs75344129717:34,958,304A/Tuncertain significance
rs15079361817:34,958,435C/Auncertain significance
rs13805629117:34,958,466C/Guncertain significance
rs144890453417:34,958,477G/Auncertain significance
rs74773463217:34,958,478G/Auncertain significance
rs78059670817:34,958,574G/Auncertain significance
rs7894330817:34,958,598G/Cbenign
rs141086959917:34,958,639G/Tuncertain significance
rs13825845817:34,958,743C/Gbenign
rs54592773517:34,958,753G/Cuncertain significance
rs36764943117:34,958,996C/Tuncertain significance
rs74946026217:34,959,064G/Auncertain significance
rs131456269917:34,964,126G/Tuncertain significance
rs75060079817:34,964,136G/Auncertain significance
rs77657256817:34,964,155G/Auncertain significance
rs20113089117:34,964,178G/Alikely benign
rs13816831317:34,964,703G/Auncertain significance
rs251034329817:34,964,718T/Cuncertain significance
rs11186132317:34,964,729G/Tuncertain significance
rs207495040717:34,964,803C/Guncertain significance
rs251034374717:34,964,841A/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.