MTCH2

mitochondrial carrier 2

Summary

This gene encodes a member of the SLC25 family of nuclear-encoded transporters that are localized in the inner mitochondrial membrane. Members of this superfamily are involved in many metabolic pathways and cell functions. Genome-wide association studies in human have identified single-nucleotide polymorphisms in several loci associated with obesity. This gene is one such locus, which is highly expressed in white adipose tissue and adipocytes, and thought to play a regulatory role in adipocyte differentiation and biology. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. A recent study showed this gene to be an authentic stop codon readthrough target that can produce two isoforms from the same mRNA by use of alternative in-frame translation termination codons. [provided by RefSeq, Dec 2017]

Known Variants29 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1076928211:47,626,492T/C
rs14723879111:47,637,815C/Tdownstream gene variant
rs74786182811:47,640,410C/Auncertain significance
rs106460811:47,640,429G/Tmissense variant
rs381733511:47,643,891T/Aintron variant
rs75155819911:47,644,320C/Guncertain significance
rs54410064111:47,647,250T/Cuncertain significance
rs475285611:47,648,042G/Aintron variant
rs77756916511:47,650,551C/Tuncertain significance
rs381733411:47,650,993C/Tintron variant
rs37314862411:47,652,135G/Auncertain significance
rs76029025511:47,652,603C/Tuncertain significance
rs14977055011:47,652,637T/Cuncertain significance
rs209730320011:47,653,247A/Guncertain significance
rs19149992411:47,656,276G/Auncertain significance
rs55855602111:47,657,101C/Tuncertain significance
rs1279457011:47,658,314C/Tintron variant
rs53550997211:47,660,325C/Tuncertain significance
rs77285247011:47,660,527A/Guncertain significance
rs76590739911:47,660,533C/Tuncertain significance
rs250985534511:47,660,548A/Cuncertain significance
rs130286676211:47,660,555G/Auncertain significance
rs77765389711:47,660,575A/Guncertain significance
rs250985560911:47,660,578G/Auncertain significance
rs712994811:47,661,498C/Aintron variant
rs1103932211:47,662,589C/Tregulatory region variant
rs1083873811:47,663,049A/Gintron variant
rs74545446711:47,663,972T/Guncertain significance
rs1103932411:47,665,686G/Aupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.