MTDH

metadherin

Summary

Enables NF-kappaB binding activity; double-stranded RNA binding activity; and transcription coactivator activity. Involved in several processes, including lipopolysaccharide-mediated signaling pathway; positive regulation of intracellular signal transduction; and regulation of DNA-templated transcription. Located in endoplasmic reticulum; nuclear lumen; and perinuclear region of cytoplasm. Implicated in hepatocellular carcinoma. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants51 total

rsidPosition (GRCh37)AllelesClassClinVar
rs12167019878:98,656,744C/Tuncertain significance
rs14801116898:98,656,801G/Auncertain significance
rs7558253638:98,656,816G/Auncertain significance
rs9127536168:98,656,849G/Auncertain significance
rs1406522378:98,656,894G/Abenign
rs9935281838:98,656,942G/Cuncertain significance
rs7783091928:98,656,949C/Tuncertain significance
rs9636286528:98,657,015C/Guncertain significance
rs7781847748:98,657,018T/Guncertain significance
rs1136461428:98,657,020C/Auncertain significance
rs5356297538:98,657,021C/Tuncertain significance
rs9654501328:98,657,030C/Tuncertain significance
rs1882716018:98,657,041C/Gbenign
rs24382078:98,666,815G/Aintron variant
rs24884380638:98,673,324G/Auncertain significance
rs24884380728:98,673,325C/Tuncertain significance
rs9194354278:98,673,381A/Guncertain significance
rs12232074258:98,673,385A/Tuncertain significance
rs24884384018:98,673,390A/Guncertain significance
rs25133698:98,681,771C/Gintron variant
rs361090388:98,689,549G/Aintron variant
rs24885371278:98,698,975A/Tuncertain significance
rs12425887958:98,699,707C/Tuncertain significance
rs7664100948:98,699,746A/Guncertain significance
rs7724526238:98,699,785G/Auncertain significance
rs18134153468:98,699,798C/Tuncertain significance
rs24885469298:98,701,280A/Guncertain significance
rs24885469648:98,701,286C/Guncertain significance
rs24885472258:98,701,328C/Guncertain significance
rs7535657098:98,703,186C/Tuncertain significance
rs7554932898:98,703,203C/Tuncertain significance
rs24885549218:98,703,290T/Clikely benign
rs1466637068:98,703,396G/Tuncertain significance
rs9316499088:98,703,403A/Guncertain significance
rs24381978:98,706,423T/A
rs5640161278:98,712,027A/Guncertain significance
rs7535431328:98,712,032G/Auncertain significance
rs14233678348:98,712,033A/Tuncertain significance
rs7751038788:98,718,914A/Tuncertain significance
rs12930097118:98,718,962T/Auncertain significance
rs1492111718:98,720,757A/T
rs7538027948:98,725,899G/Tuncertain significance
rs1458815248:98,725,927T/Cuncertain significance
rs11999726838:98,731,340C/Auncertain significance
rs13124920528:98,731,382A/Guncertain significance
rs7687956598:98,731,394G/Auncertain significance
rs12998822808:98,731,398T/Clikely benign
rs3706488458:98,735,200A/Guncertain significance
rs1170260638:98,736,822T/Cbenign
rs24878600788:98,736,828C/Auncertain significance
rs14850899318:98,736,830A/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.