MVB12B

multivesicular body subunit 12B

Summary

The protein encoded by this gene is a component of the ESCRT-I complex, a heterotetramer, which mediates the sorting of ubiquitinated cargo protein from the plasma membrane to the endosomal vesicle. ESCRT-I complex plays an essential role in HIV budding and endosomal protein sorting. Depletion and overexpression of this and related protein (MVB12A) inhibit HIV-1 infectivity and induce unusual viral assembly defects, indicating a role for MVB12 subunits in regulating ESCRT-mediated virus budding. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Aug 2011]

Known Variants29 total

rsidPosition (GRCh37)AllelesClassClinVar
rs18881569:129,102,840A/Gbenign
rs3705269449:129,102,844A/Guncertain significance
rs7505281549:129,102,850C/Guncertain significance
rs3762236579:129,102,880C/Tuncertain significance
rs12003816289:129,102,899G/Auncertain significance
rs22868899:129,143,435A/Gbenign
rs18308007779:129,148,863T/Cuncertain significance
rs1420767319:129,148,916A/Guncertain significance
rs736680189:129,151,884C/Tintron variant
rs1389997099:129,154,403G/Alikely benign
rs96960009:129,154,426G/Auncertain significance
rs7772344989:129,154,455C/Guncertain significance
rs1843168119:129,157,850A/Glikely benign
rs1410171389:129,157,928C/Tuncertain significance
rs7565085879:129,157,929G/Alikely benign
rs2001095209:129,157,967A/Cuncertain significance
rs7744385539:129,184,168G/Tuncertain significance
rs1447636239:129,184,186C/Tuncertain significance
rs14909770589:129,184,194G/Auncertain significance
rs771122389:129,187,603A/Gupstream gene variant
rs7589709:129,194,773A/C
rs1809891249:129,232,278T/Cintron variant
rs48365449:129,236,355C/Tintron variant
rs3769295049:129,246,242G/Alikely benign
rs22868859:129,246,487A/T
rs70277989:129,257,152C/A
rs7689635599:129,265,446G/Alikely benign
rs7726511099:129,265,471C/Guncertain significance
rs626400449:129,265,500C/Tbenign

Gene information from NCBI Gene. Variant classifications from ClinVar.