NDUFA3

NADH:ubiquinone oxidoreductase subunit A3

Summary

Predicted to enable NADH dehydrogenase (ubiquinone) activity. Predicted to be involved in mitochondrial electron transport, NADH to ubiquinone and proton motive force-driven mitochondrial ATP synthesis. Located in mitochondrial inner membrane. Part of respiratory chain complex I. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants6 total

rsidPosition (GRCh37)AllelesClassClinVar
rs15061780919:54,606,436C/Auncertain significance
rs116828104319:54,606,484G/Alikely benign
rs18869744019:54,606,964A/Gdownstream gene variant
rs75169665419:54,609,244T/Auncertain significance
rs14938310319:54,609,265C/Tuncertain significance
rs18406426819:54,609,374G/Adownstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.