NFX1

nuclear transcription factor, X-box binding 1

Summary

MHC class II gene expression is controlled primarily at the transcriptional level by transcription factors that bind to the X and Y boxes, two highly conserved elements in the proximal promoter of MHC class II genes. The protein encoded by this gene is a transcriptional repressor capable of binding to the conserved X box motif of HLA-DRA and other MHC class II genes in vitro. The protein may play a role in regulating the duration of an inflammatory response by limiting the period in which class II MHC molecules are induced by IFN-gamma. Three alternative splice variants, each of which encodes a different isoform, have been identified. [provided by RefSeq, Jul 2008]

Known Variants52 total

rsidPosition (GRCh37)AllelesClassClinVar
rs7786195919:33,290,586C/Auncertain significance
rs7582634949:33,294,353G/A
rs8893793819:33,294,426A/Guncertain significance
rs12575775159:33,294,452C/Guncertain significance
rs7730053529:33,294,526G/Cuncertain significance
rs7607269439:33,294,532A/Cuncertain significance
rs1503302159:33,294,544C/Tuncertain significance
rs2004087919:33,294,549C/Tuncertain significance
rs7790780049:33,294,594G/Cuncertain significance
rs7523765819:33,294,616C/Tuncertain significance
rs1380328389:33,294,636A/Cuncertain significance
rs7805684579:33,294,646C/Tuncertain significance
rs3718513479:33,294,742G/Cuncertain significance
rs24893813609:33,295,215A/Guncertain significance
rs1508438799:33,295,288A/Guncertain significance
rs1396341839:33,295,316G/Cuncertain significance
rs7512978089:33,295,344C/Tuncertain significance
rs7473335869:33,295,398G/Auncertain significance
rs12512180089:33,295,410G/Tuncertain significance
rs7548939229:33,301,385A/Guncertain significance
rs7551338799:33,303,234C/Tuncertain significance
rs24894196919:33,307,258A/Glikely benign
rs14185105919:33,307,262A/Tuncertain significance
rs18219445899:33,311,132T/Auncertain significance
rs2005305069:33,313,688C/Guncertain significance
rs24894553669:33,313,714T/Guncertain significance
rs7537130769:33,313,785A/Tuncertain significance
rs8312779:33,314,973A/Tintron variant
rs5612445599:33,318,750C/Tuncertain significance
rs7557238179:33,318,773G/Auncertain significance
rs1445226029:33,318,778A/Glikely benign
rs24894870779:33,319,018C/Tuncertain significance
rs344443649:33,319,045G/Auncertain significance
rs1429038589:33,319,114G/Auncertain significance
rs625427249:33,324,542T/Gintron variant
rs24895366869:33,328,617G/Auncertain significance
rs1860444389:33,338,558C/Tuncertain significance
rs1995500839:33,342,822C/Tuncertain significance
rs7587843769:33,347,036T/Cuncertain significance
rs7507943089:33,351,561C/Tuncertain significance
rs752311969:33,351,709C/Guncertain significance
rs1478184729:33,352,682G/Alikely benign
rs1435595919:33,354,178C/Guncertain significance
rs14020147609:33,354,862G/Auncertain significance
rs1841231929:33,356,166A/Gupstream gene variant
rs18241188139:33,364,707A/Guncertain significance
rs7454019779:33,366,642A/Cuncertain significance
rs3729282329:33,366,747C/Guncertain significance
rs3747110069:33,366,751A/Guncertain significance
rs1447873399:33,367,523G/Alikely benign
rs13639939109:33,369,921A/Guncertain significance
rs10110342899:33,369,941G/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.