NLRP9

NLR family pyrin domain containing 9

Summary

The protein encoded by this gene belongs to the NALP protein family. Members of the NALP protein family typically contain a NACHT domain, a NACHT-associated domain (NAD), a C-terminal leucine-rich repeat (LRR) region, and an N-terminal pyrin domain (PYD). This protein may play a regulatory role in the innate immune system as similar family members belong to the signal-induced multiprotein complex, the inflammasome, that activates the pro-inflammatory caspases, caspase-1 and caspase-5. [provided by RefSeq, Jul 2008]

Known Variants75 total

rsidPosition (GRCh37)AllelesClassClinVar
rs36789278019:56,220,310C/Tuncertain significance
rs75335642719:56,220,311G/Alikely benign
rs15101799419:56,221,458T/Adownstream gene variant
rs19947623119:56,223,138C/Tnot provided
rs19947585019:56,223,257G/Tuncertain significance
rs14851107719:56,223,314A/Guncertain significance
rs77272736819:56,223,322G/Auncertain significance
rs19947623019:56,223,672G/Anot provided
rs14609879419:56,223,788G/Abenign
rs37399060819:56,223,795T/Auncertain significance
rs78047674019:56,223,796C/Guncertain significance
rs75686395619:56,223,915A/Guncertain significance
rs19947622919:56,223,996G/Cnot provided
rs7393331719:56,226,457G/Abenign
rs55954438619:56,226,470A/Guncertain significance
rs77848206019:56,226,490A/Guncertain significance
rs19947622819:56,227,351C/Anot provided
rs13849652019:56,228,104C/Tbenign
rs37406174419:56,228,215C/Auncertain significance
rs76325330019:56,235,407A/Tlikely benign
rs20213089719:56,235,416G/Tuncertain significance
rs20134914119:56,235,417G/Tuncertain significance
rs37503194019:56,235,425C/Tuncertain significance
rs77231352319:56,235,500C/Guncertain significance
rs77612883019:56,241,315A/Tuncertain significance
rs15098265219:56,241,332C/Tuncertain significance
rs75139023219:56,241,333G/Auncertain significance
rs20024329919:56,241,342C/Tuncertain significance
rs20128760419:56,241,353T/Cuncertain significance
rs251435220819:56,243,408A/Cuncertain significance
rs37585861119:56,243,422G/Cuncertain significance
rs14624016619:56,243,435A/Glikely benign
rs36830476519:56,243,437T/Cuncertain significance
rs77974686319:56,243,486A/Guncertain significance
rs20076729619:56,243,492A/Guncertain significance
rs75353773619:56,243,521G/Auncertain significance
rs37600615219:56,243,559G/Cuncertain significance
rs14905887619:56,243,611C/Auncertain significance
rs140424657419:56,243,672T/Guncertain significance
rs14378817619:56,243,714T/Clikely benign
rs36967426819:56,243,789T/Auncertain significance
rs14689652819:56,243,804C/Tuncertain significance
rs251435279819:56,243,832C/Tuncertain significance
rs7361526719:56,243,859C/Abenign
rs76888769419:56,243,874A/Cuncertain significance
rs129245293819:56,243,900G/Auncertain significance
rs20120923619:56,243,909C/Tuncertain significance
rs54304144119:56,243,937T/Auncertain significance
rs56325617419:56,243,947C/Tuncertain significance
rs19947584919:56,243,979A/Gnot provided
rs76336024719:56,244,077T/Cuncertain significance
rs19947584819:56,244,141C/Gnot provided
rs19947584719:56,244,175C/Anot provided
rs251435350419:56,244,202A/Tuncertain significance
rs78076541619:56,244,238A/Glikely benign
rs100304466619:56,244,295G/Auncertain significance
rs77500701019:56,244,401G/Auncertain significance
rs156860412919:56,244,424C/Tuncertain significance
rs75323170419:56,244,463T/Cuncertain significance
rs198864765519:56,244,478T/Cuncertain significance
rs37103416019:56,244,522G/Cuncertain significance
rs77849843919:56,244,557C/Tuncertain significance
rs77365665419:56,244,763C/Tuncertain significance
rs37027400519:56,244,767T/Clikely benign
rs20117322219:56,244,779T/Clikely benign
rs5623579019:56,244,783T/Cbenign
rs14250267519:56,244,796T/Cuncertain significance
rs92771770219:56,244,833G/Auncertain significance
rs4559743619:56,244,837A/Gbenign
rs251435985519:56,249,520T/Clikely benign
rs14273050519:56,249,579A/Gbenign
rs251436001819:56,249,604T/Auncertain significance
rs18360702819:56,249,630A/Clikely benign
rs136952122119:56,249,653G/Auncertain significance
rs19947584619:56,249,721G/Anot provided

Gene information from NCBI Gene. Variant classifications from ClinVar.