OTUB2

OTU deubiquitinase, ubiquitin aldehyde binding 2

Summary

This gene encodes one of several deubiquitylating enzymes. Ubiquitin modification of proteins is needed for their stability and function; to reverse the process, deubiquityling enzymes remove ubiquitin. This protein contains an OTU domain and binds Ubal (ubiquitin aldehyde); an active cysteine protease site is present in the OTU domain. [provided by RefSeq, Aug 2011]

Known Variants19 total

rsidPosition (GRCh37)AllelesClassClinVar
rs18115744314:94,497,969T/Gintron variant
rs76025166814:94,503,807C/Tuncertain significance
rs14480370214:94,503,808G/Alikely benign
rs75347613714:94,503,811G/Auncertain significance
rs77739580314:94,505,312C/Guncertain significance
rs37184024214:94,505,320A/Cuncertain significance
rs3457438114:94,505,330G/Auncertain significance
rs74618893514:94,505,336C/Tuncertain significance
rs77453967814:94,505,351G/Cuncertain significance
rs37497236614:94,510,327C/Tuncertain significance
rs77041312914:94,510,953G/Auncertain significance
rs77902639414:94,511,044C/Tuncertain significance
rs75911301314:94,511,064C/Guncertain significance
rs74619802514:94,511,088A/Guncertain significance
rs74663888114:94,511,116T/Auncertain significance
rs77355325514:94,512,081C/Tlikely benign
rs76359840214:94,512,155G/Auncertain significance
rs37190041714:94,512,182G/Auncertain significance
rs145808856014:94,512,204C/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.