PCOLCE

procollagen C-endopeptidase enhancer

Summary

Fibrillar collagen types I-III are synthesized as precursor molecules known as procollagens. These precursors contain amino- and carboxyl-terminal peptide extensions known as N- and C-propeptides, respectively, which are cleaved, upon secretion of procollagen from the cell, to yield the mature triple helical, highly structured fibrils. This gene encodes a glycoprotein which binds and drives the enzymatic cleavage of type I procollagen and heightens C-proteinase activity. [provided by RefSeq, Jul 2008]

Known Variants28 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1424218117:100,200,096C/Guncertain significance
rs1512684137:100,200,099C/Auncertain significance
rs7519185077:100,200,151G/Cuncertain significance
rs1382996037:100,201,082A/Tuncertain significance
rs7599817847:100,201,132C/Guncertain significance
rs7677655687:100,201,136A/Guncertain significance
rs1883774647:100,201,149C/Guncertain significance
rs24860686977:100,201,589A/Guncertain significance
rs14687182647:100,201,633C/Auncertain significance
rs7805600897:100,201,639C/Guncertain significance
rs5768899287:100,201,669T/Cuncertain significance
rs7515159967:100,201,682G/Cuncertain significance
rs7693564967:100,201,751A/Guncertain significance
rs24860716477:100,202,805C/Guncertain significance
rs13992044437:100,202,831C/Glikely benign
rs1489432307:100,203,380G/Tuncertain significance
rs3741186087:100,204,135G/Alikely benign
rs7503692237:100,204,136C/Alikely benign
rs7725128007:100,204,175C/Tuncertain significance
rs9853327777:100,204,191A/Guncertain significance
rs7573432527:100,204,221C/Tuncertain significance
rs1462099787:100,205,261G/Abenign
rs2006577957:100,205,607G/Alikely benign
rs24860760837:100,205,639C/Auncertain significance
rs1126852117:100,205,641G/Auncertain significance
rs8912901217:100,205,700G/Cuncertain significance
rs1175956007:100,205,703C/Tbenign
rs617395567:100,205,706G/Cbenign

Gene information from NCBI Gene. Variant classifications from ClinVar.