PDXK

pyridoxal kinase

Summary

The protein encoded by this gene phosphorylates vitamin B6, a step required for the conversion of vitamin B6 to pyridoxal-5-phosphate, an important cofactor in intermediary metabolism. The encoded protein is cytoplasmic and probably acts as a homodimer. Alternatively spliced transcript variants have been described, but their biological validity has not been determined. [provided by RefSeq, Jul 2008]

Known Variants51 total

rsidPosition (GRCh37)AllelesClassClinVar
rs6222917921:45,138,930G/Tbenign
rs52736278321:45,139,013A/Gbenign
rs1305030721:45,153,751A/Gbenign
rs127458386721:45,153,985C/Glikely benign
rs229980621:45,154,144T/Cbenign
rs13918086821:45,157,062C/Tlikely benign
rs74915445521:45,157,169G/Alikely benign
rs7645907921:45,161,346G/Abenign
rs7337521621:45,161,432A/Gbenign
rs14048591521:45,161,433T/Cbenign
rs148695742921:45,161,448C/Tuncertain significance
rs54330433621:45,161,553G/Auncertain significance
rs74620857221:45,161,625A/Glikely benign
rs160181423821:45,161,630T/Alikely pathogenic
rs7390837721:45,161,850T/Cbenign
rs14478620021:45,163,612G/Alikely benign
rs74554301021:45,163,646A/Guncertain significance
rs11459395821:45,163,714T/Gbenign
rs7337521821:45,163,766G/Abenign
rs7437356821:45,163,867G/Tbenign
rs7773457621:45,166,002C/Tlikely benign
rs14726313521:45,166,005T/Cuncertain significance
rs57386877421:45,166,165A/G
rs11359775021:45,168,709C/Tbenign
rs1153953421:45,168,884A/Gbenign
rs141079246021:45,168,904A/Guncertain significance
rs11257928421:45,168,914A/Glikely benign
rs6173706221:45,168,923G/Abenign
rs997482721:45,169,005G/Abenign
rs110679721:45,170,285G/Abenign
rs76814563921:45,170,425G/Auncertain significance
rs107926821:45,170,580G/Abenign
rs813450721:45,172,379G/Abenign
rs74727555321:45,172,435G/Auncertain significance
rs201079521:45,172,628G/Aintron variantbenign
rs813209721:45,173,231C/Abenign
rs20154647921:45,173,472G/Auncertain significance
rs75662781221:45,173,479C/Guncertain significance
rs812733521:45,173,480C/Tbenign
rs36792714221:45,173,484G/Auncertain significance
rs75933379621:45,173,500G/Apathogenic
rs75748051621:45,173,523G/Apathogenic
rs7769944721:45,173,705C/Tbenign
rs207053421:45,175,370A/Gbenign
rs812863921:45,175,571C/Abenign
rs118493796621:45,175,832C/Tuncertain significance
rs14632196321:45,175,839C/Tlikely benign
rs20087580721:45,175,847G/Auncertain significance
rs78138942721:45,175,880G/Auncertain significance
rs104740221:45,175,952G/Abenign
rs752721:45,175,958T/Cbenign

Gene information from NCBI Gene. Variant classifications from ClinVar.