PET100

PET100 cytochrome c oxidase chaperone

Summary

Mitochondrial complex IV, or cytochrome c oxidase, is a large transmembrane protein complex that is part of the respiratory electron transport chain of mitochondria. The small protein encoded by this gene plays a role in the biogenesis of mitochondrial complex IV. This protein localizes to the inner mitochondrial membrane and is exposed to the intermembrane space. Mutations in this gene are associated with mitochondrial complex IV deficiency. This gene has a pseudogene on chromosome 3. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Apr 2014]

Known Variants78 total

rsidPosition (GRCh37)AllelesClassClinVar
rs413481019:7,694,349C/Tlikely benign
rs413480919:7,694,393G/Abenign
rs413480819:7,694,538A/Gbenign
rs7392147719:7,694,585G/Tbenign
rs79408519:7,694,602C/Gbenign
rs376067519:7,694,662T/Cbenign
rs105752268219:7,694,701G/Clikely benign
rs100160385219:7,694,717G/Alikely benign
rs97739251219:7,694,720A/Tpathogenic
rs203123336419:7,694,737G/Alikely benign
rs251266194519:7,694,756C/Tlikely benign
rs138404082619:7,694,757A/Glikely benign
rs203123458919:7,694,760G/Alikely benign
rs98970824819:7,694,761G/Alikely benign
rs11535707919:7,695,266G/Cbenign
rs376067619:7,695,336A/Gbenign
rs413480519:7,695,441C/Tlikely benign
rs251266335319:7,695,445C/Glikely benign
rs203125769319:7,695,457A/Glikely pathogenic
rs131119310519:7,695,470C/Apathogenic
rs203125886519:7,695,497G/Apathogenic
rs18432585419:7,695,505A/Glikely benign
rs413480419:7,695,513G/Cuncertain significance
rs117200439319:7,695,546G/Alikely pathogenic
rs96339718419:7,695,549G/Auncertain significance
rs75355491519:7,695,552A/Gconflicting classifications of pathogenicity
rs251266361619:7,695,559G/Alikely benign
rs214619308819:7,695,561G/Clikely benign
rs251266362919:7,695,563G/Alikely benign
rs1126000419:7,695,620T/Cbenign
rs11762260219:7,695,636T/Alikely benign
rs14829638719:7,695,681G/Alikely benign
rs105158862419:7,695,700T/Clikely benign
rs145943789019:7,695,706C/Gconflicting classifications of pathogenicity
rs251266409419:7,695,708G/Alikely pathogenic
rs203126645419:7,695,733G/Tuncertain significance
rs75632614719:7,695,735A/Tuncertain significance
rs203126695319:7,695,743T/Clikely benign
rs251266418019:7,695,747C/Tlikely benign
rs11563573019:7,695,758A/Glikely benign
rs1188182019:7,695,841A/Gbenign
rs376067719:7,695,977C/Gbenign
rs1188219719:7,696,138G/Abenign
rs11312465419:7,696,198G/Alikely benign
rs7392147919:7,696,260G/Alikely benign
rs54761646719:7,696,341C/Tlikely benign
rs139280900319:7,696,342C/Tlikely benign
rs141117191919:7,696,343G/Tlikely benign
rs105752229419:7,696,344C/Tlikely benign
rs251266581419:7,696,349C/Tlikely benign
rs251266582019:7,696,350C/Tlikely benign
rs135566594519:7,696,352C/Tlikely benign
rs251266585019:7,696,355C/Glikely benign
rs251266586519:7,696,359C/Tuncertain significance
rs130334259319:7,696,361T/Clikely benign
rs100350500619:7,696,380A/Cuncertain significance
rs75620125719:7,696,392C/Tuncertain significance
rs76428872219:7,696,393G/Auncertain significance
rs75407118719:7,696,394G/Alikely benign
rs75738827519:7,696,398C/Tuncertain significance
rs77924353319:7,696,399G/Aconflicting classifications of pathogenicity
rs96864402119:7,696,401C/Tuncertain significance
rs97721992619:7,696,404G/Tuncertain significance
rs74620453119:7,696,405A/Tuncertain significance
rs122216405719:7,696,406G/Alikely benign
rs118664966019:7,696,413C/Tuncertain significance
rs57062017719:7,696,417T/Cconflicting classifications of pathogenicity
rs123304964719:7,696,418T/Clikely benign
rs11766171519:7,696,419C/Tbenign
rs55638045119:7,696,420G/Aconflicting classifications of pathogenicity
rs37596893519:7,696,421C/Tlikely benign
rs76810998619:7,696,424C/Tlikely benign
rs203130267519:7,696,427C/Tlikely benign
rs251266609819:7,696,436C/Tlikely benign
rs127091155719:7,696,438C/Glikely benign
rs136136001819:7,696,441G/Alikely benign
rs11460085819:7,696,496G/Tlikely benign
rs11236778119:7,696,678C/Tlikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.