PIPOX

pipecolic acid and sarcosine oxidase

Summary

Enables L-pipecolate oxidase activity and sarcosine oxidase activity. Involved in L-lysine catabolic process to acetyl-CoA via L-pipecolate. Located in peroxisome. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants22 total

rsidPosition (GRCh37)AllelesClassClinVar
rs74765779517:27,370,248C/Tuncertain significance
rs721137517:27,371,788G/Cintron variant
rs14491864817:27,371,913C/Guncertain significance
rs77384901117:27,371,935C/Tuncertain significance
rs74743314717:27,372,003G/Auncertain significance
rs254540096817:27,380,084G/Cuncertain significance
rs75658515617:27,380,110G/Auncertain significance
rs77072708417:27,380,131A/Guncertain significance
rs78082511317:27,380,149C/Guncertain significance
rs37588740117:27,380,462G/Alikely benign
rs18581737017:27,380,494G/Auncertain significance
rs75504497217:27,381,657G/Alikely benign
rs78150475917:27,382,144G/Tuncertain significance
rs20012761817:27,382,150G/Alikely benign
rs136997840017:27,382,213G/Auncertain significance
rs125206313317:27,382,235A/Guncertain significance
rs76758651617:27,382,862G/Auncertain significance
rs75976552817:27,383,198G/Auncertain significance
rs75121942317:27,383,210G/Auncertain significance
rs37550301817:27,383,216G/Auncertain significance
rs78082716217:27,383,222G/Auncertain significance
rs15068736217:27,383,283G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.