PKD1L2

polycystin 1 like 2 (gene/pseudogene)

Summary

This gene encodes a member of the polycystin protein family. This protein may function as a G-protein-coupled component or regulator of cation channel pores. The long isoform of this protein contains 11 transmembrane domains, a latrophilin/CL-1-like GPCR proteolytic site (GPS) domain, and a polycystin-1, lipoxygenase, alpha-toxin (PLAT) domain. Alternative splicing results in multiple transcript variants encoding distinct isoforms. This gene is a polymorphic pseudogene in humans. [provided by RefSeq, May 2022]

Known Variants214 total

rsidPosition (GRCh37)AllelesClassClinVar
rs488812416:81,143,961A/Tcoding sequence variant
rs805915316:81,145,675T/Ccoding sequence variant
rs488924016:81,156,522T/Cintron variant
rs20083996016:81,157,321G/Clikely pathogenic
rs20029112716:81,164,066G/Tuncertain significance
rs37147528016:81,164,105G/Auncertain significance
rs76146893616:81,164,196G/Auncertain significance
rs137580538716:81,164,220G/Tuncertain significance
rs37497772416:81,164,226G/Cuncertain significance
rs20041190016:81,167,213G/Tuncertain significance
rs36852427816:81,167,231C/Tuncertain significance
rs250786115516:81,167,251G/Auncertain significance
rs75835833516:81,167,258A/Guncertain significance
rs75106129116:81,167,265C/Auncertain significance
rs37207136616:81,167,268G/Tlikely benign
rs14168632116:81,168,423T/Cregulatory region variant
rs134934945316:81,171,063G/Cuncertain significance
rs197412694916:81,171,084C/Tuncertain significance
rs37176507716:81,171,126C/Guncertain significance
rs134646057216:81,173,121G/Auncertain significance
rs102438691616:81,173,141T/Cuncertain significance
rs75436920916:81,173,154C/Tuncertain significance
rs141074239516:81,173,158C/Tlikely benign
rs75280768416:81,173,188C/Auncertain significance
rs145513981616:81,173,202G/Tuncertain significance
rs117137746716:81,173,204C/Tuncertain significance
rs75370667116:81,174,911G/Tuncertain significance
rs215183628616:81,181,002C/Tuncertain significance
rs250791503316:81,181,005C/Auncertain significance
rs123663259816:81,181,014A/Cuncertain significance
rs11369659416:81,181,065C/Guncertain significance
rs116907618216:81,181,085G/Cuncertain significance
rs36985287316:81,181,104C/Tuncertain significance
rs75373796916:81,181,764G/Auncertain significance
rs37530064016:81,181,806T/Auncertain significance
rs75428866316:81,181,842T/Cuncertain significance
rs75542075116:81,181,843C/Tuncertain significance
rs26760465516:81,181,854C/Tuncertain significance
rs91438350316:81,181,858G/Auncertain significance
rs54144589616:81,181,956A/Guncertain significance
rs53036723116:81,183,339A/Guncertain significance
rs37323964416:81,183,341C/Tuncertain significance
rs37703159016:81,183,402C/Tuncertain significance
rs53213132816:81,183,438G/Auncertain significance
rs74989572616:81,183,446G/Cuncertain significance
rs250792544816:81,183,456T/Auncertain significance
rs37181716516:81,183,469C/Tlikely benign
rs18801099916:81,183,492T/Guncertain significance
rs37759440716:81,185,396G/Auncertain significance
rs91450358316:81,185,424C/Tuncertain significance
rs92458349616:81,185,466A/Guncertain significance
rs52768844016:81,185,477C/Tlikely benign
rs37425487316:81,185,478G/Cuncertain significance
rs18402445716:81,185,514C/Tuncertain significance
rs76997960516:81,187,575C/Tlikely benign
rs105651249216:81,187,579C/Guncertain significance
rs77846153716:81,187,611C/Tlikely benign
rs37188175616:81,187,708C/Tuncertain significance
rs140340173516:81,187,844T/Cuncertain significance
rs77912320716:81,187,846G/Auncertain significance
rs75884512716:81,187,918T/Cuncertain significance
rs127044676316:81,187,943C/Tuncertain significance
rs76502678816:81,190,486T/Cuncertain significance
rs37581357316:81,190,514C/Tuncertain significance
rs197495093216:81,190,520C/Auncertain significance
rs76952653316:81,190,547C/Tuncertain significance
rs20055988816:81,190,634C/Tuncertain significance
rs76096907616:81,190,649G/Auncertain significance
rs36894403816:81,190,685G/Auncertain significance
rs118832954216:81,190,694C/Tuncertain significance
rs7980950716:81,193,237C/Guncertain significance
rs144124895516:81,193,278C/Tuncertain significance
rs37103513916:81,193,308G/Auncertain significance
rs250797145416:81,193,356G/Auncertain significance
rs18146989116:81,193,378C/Tuncertain significance
rs77948518816:81,193,393G/Clikely benign
rs20169161216:81,193,410G/Auncertain significance
rs37425733616:81,194,320G/Tuncertain significance
rs19983938916:81,194,324C/Tuncertain significance
rs37083705516:81,194,338T/Cuncertain significance
rs37290022916:81,194,347T/Cuncertain significance
rs94215171816:81,194,377A/Guncertain significance
rs7963251316:81,194,378T/Cuncertain significance
rs13934500916:81,194,383G/Auncertain significance
rs76937280516:81,194,397C/Auncertain significance
rs101529469416:81,194,497C/Tuncertain significance
rs37447343816:81,194,498G/Auncertain significance
rs78166272416:81,197,207C/Tuncertain significance
rs20088142116:81,197,216C/Guncertain significance
rs127793865516:81,197,245C/Tuncertain significance
rs20012081416:81,197,248C/Tuncertain significance
rs76479344116:81,197,263C/Tuncertain significance
rs76615954716:81,197,333T/Cuncertain significance
rs94172475216:81,198,252T/Cuncertain significance
rs144307506816:81,198,280A/Guncertain significance
rs130463425516:81,198,290G/Cuncertain significance
rs36918265616:81,198,347A/Guncertain significance
rs105409183116:81,199,451T/Auncertain significance
rs1259704016:81,199,555A/Gbenign
rs132673309416:81,201,530G/Cuncertain significance

Showing 100 of 214 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.