PKNOX2

PBX/knotted 1 homeobox 2

Summary

Homeodomain proteins are sequence-specific transcription factors that share a highly conserved DNA-binding domain and play fundamental roles in cell proliferation, differentiation, and death. PKNOX2 belongs to the TALE (3-amino acid loop extension) class of homeodomain proteins characterized by a 3-amino acid extension between alpha helices 1 and 2 within the homeodomain (Imoto et al., 2001 [PubMed 11549286]).[supplied by OMIM, Oct 2009]

Known Variants27 total

rsidPosition (GRCh37)AllelesClassClinVar
rs18597115211:125,035,059C/Gregulatory region variant
rs61732511:125,068,880A/C
rs68186411:125,078,396C/Gintron variant
rs142615311:125,170,639A/Gregulatory region variant
rs75033811:125,172,593A/C
rs1089336611:125,178,403C/Tintron variant
rs1228459411:125,179,853A/T
rs11161574811:125,219,773A/Gregulatory region variant
rs37172237711:125,237,775C/Guncertain significance
rs195228000011:125,237,821T/Cuncertain significance
rs20121398311:125,237,835A/Cuncertain significance
rs195228422011:125,237,860C/Auncertain significance
rs36994949911:125,237,869G/Auncertain significance
rs1227335011:125,241,046G/Aintron variant
rs249734948811:125,255,551A/Cuncertain significance
rs249735024311:125,255,611A/Guncertain significance
rs249745895211:125,267,905G/Tuncertain significance
rs711236511:125,277,494C/Tintron variant
rs75784554111:125,280,171T/Auncertain significance
rs77884940411:125,280,200G/Auncertain significance
rs77103755611:125,280,683T/Guncertain significance
rs92923234611:125,280,746G/Auncertain significance
rs126955142411:125,281,729A/Cuncertain significance
rs20059007611:125,300,013G/Auncertain significance
rs74999181711:125,301,062G/Tuncertain significance
rs95449829211:125,301,067A/Guncertain significance
rs146299349811:125,301,076G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.