PKP3

plakophilin 3

Summary

This gene encodes a member of the arm-repeat (armadillo) and plakophilin gene families. Plakophilin proteins contain numerous armadillo repeats, localize to cell desmosomes and nuclei, and participate in linking cadherins to intermediate filaments in the cytoskeleton. This protein may act in cellular desmosome-dependent adhesion and signaling pathways. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Dec 2014]

Known Variants103 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14372894011:392,702G/Alikely benign
rs77389946911:394,299G/Auncertain significance
rs96983849511:394,321C/Tuncertain significance
rs75360725711:394,354C/Tuncertain significance
rs91300593111:394,387G/Auncertain significance
rs141046365411:394,389G/Auncertain significance
rs105202737511:394,410C/Tuncertain significance
rs89067656311:394,417G/Auncertain significance
rs103635939011:394,423C/Tuncertain significance
rs11376512111:394,446G/Auncertain significance
rs96132667311:394,477G/Auncertain significance
rs103605595011:394,485G/Auncertain significance
rs37314227511:394,491G/Auncertain significance
rs98763688811:394,523A/Cuncertain significance
rs1090215811:396,308G/Aregulatory region variant
rs710584811:396,546G/Aregulatory region variant
rs15073889111:396,674G/Auncertain significance
rs14939698211:396,686C/Tuncertain significance
rs54426990711:396,821G/Auncertain significance
rs131832928911:396,823C/Guncertain significance
rs14636606211:396,865C/Tbenign
rs57441822411:396,866G/Auncertain significance
rs74557597811:396,871G/Tuncertain significance
rs37369197411:396,874G/Auncertain significance
rs155491857011:396,892C/Tuncertain significance
rs37433788411:396,893G/Auncertain significance
rs20093370311:396,946G/Cuncertain significance
rs253926378511:396,947G/Cuncertain significance
rs37593762911:396,978C/Tlikely benign
rs77469953311:396,982C/Tuncertain significance
rs20213655611:396,985G/Auncertain significance
rs14449937011:397,019G/Auncertain significance
rs77455822611:397,042C/Auncertain significance
rs77257583611:397,046G/Auncertain significance
rs15126557311:397,054C/Tlikely benign
rs14050931311:397,055G/Tuncertain significance
rs77901906811:397,070G/Auncertain significance
rs20087735311:397,078G/Auncertain significance
rs77127731811:397,081C/Tuncertain significance
rs20198235311:397,143G/Alikely benign
rs19993500911:397,147G/Auncertain significance
rs76139293111:397,198G/Auncertain significance
rs78173903111:397,222C/Tuncertain significance
rs53219666111:397,228A/Tuncertain significance
rs77166519211:397,232G/Auncertain significance
rs36810012311:397,283G/Auncertain significance
rs77082603411:397,288G/Auncertain significance
rs76777539111:397,312G/Alikely benign
rs77043823611:397,337C/Tuncertain significance
rs37309853611:397,373C/Tuncertain significance
rs7775221511:397,390G/Tbenign
rs57352226211:397,411G/Cuncertain significance
rs76325253611:397,444G/Auncertain significance
rs76925592711:397,564G/Auncertain significance
rs156487936011:397,568T/Cuncertain significance
rs146487815711:397,592C/Guncertain significance
rs184707154011:397,595A/Guncertain significance
rs253926529811:397,601A/Guncertain significance
rs57133719311:397,639A/Cuncertain significance
rs13866210211:397,642G/Tuncertain significance
rs76748512011:399,013C/Tuncertain significance
rs74889075611:399,061C/Tuncertain significance
rs77316769911:399,079C/Tuncertain significance
rs76041584811:399,080G/Auncertain significance
rs75675132911:399,161G/Auncertain significance
rs14614838711:399,172G/Tuncertain significance
rs77741135211:399,182G/Auncertain significance
rs144426791011:400,020G/Auncertain significance
rs14047996411:400,064G/Alikely benign
rs14444733311:400,075G/Auncertain significance
rs13912810011:400,124C/Glikely benign
rs79626053711:400,374C/Tuncertain significance
rs88839747611:400,432C/Guncertain significance
rs95050950611:400,538G/Tuncertain significance
rs36921612511:400,577C/Auncertain significance
rs138955335911:400,593T/Cuncertain significance
rs105417056911:400,629G/Auncertain significance
rs119498137911:400,695G/Tuncertain significance
rs120241641411:400,703G/Cuncertain significance
rs11378464211:403,087G/Alikely benign
rs53861423511:403,097C/Tuncertain significance
rs37745854211:403,098G/Tlikely benign
rs76811892011:403,157A/Tuncertain significance
rs75346913511:403,177C/Tuncertain significance
rs77855165011:403,189C/Tuncertain significance
rs74759683811:403,190G/Auncertain significance
rs37297452011:403,214C/Tuncertain significance
rs77770305911:403,255G/Auncertain significance
rs20124887511:403,622C/Tuncertain significance
rs14085199911:403,627G/Auncertain significance
rs37032782011:403,636C/Tuncertain significance
rs14765773511:403,658G/Cuncertain significance
rs37596468411:403,696G/Auncertain significance
rs11663346611:403,749C/Tbenign
rs20222746311:403,981G/Amissense variant
rs55496215011:403,987G/Auncertain significance
rs20103693611:404,000C/Tuncertain significance
rs20165488411:404,054T/Cuncertain significance
rs77867339311:404,068G/Auncertain significance
rs100453686511:404,069C/Tuncertain significance

Showing 100 of 103 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.