PLAG1

PLAG1 zinc finger

Summary

Pleomorphic adenoma gene 1 encodes a zinc finger protein with 2 putative nuclear localization signals. PLAG1, which is developmentally regulated, has been shown to be consistently rearranged in pleomorphic adenomas of the salivary glands. PLAG1 is activated by the reciprocal chromosomal translocations involving 8q12 in a subset of salivary gland pleomorphic adenomas. Three transcript variants encoding two different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]

Known Variants30 total

rsidPosition (GRCh37)AllelesClassClinVar
rs12591642018:57,078,844G/Cuncertain significance
rs24871033518:57,078,848A/Cuncertain significance
rs5595247538:57,078,897T/Cuncertain significance
rs1445523728:57,078,932G/Cuncertain significance
rs358831568:57,078,933G/Tbenign
rs751086318:57,078,948C/Glikely benign
rs7658251148:57,078,959G/Auncertain significance
rs7529283018:57,079,044A/Cuncertain significance
rs1414078638:57,079,077G/Auncertain significance
rs7767085028:57,079,092T/Cuncertain significance
rs24871045708:57,079,150A/Clikely benign
rs13608196038:57,079,244C/Tuncertain significance
rs7712284818:57,079,403G/Auncertain significance
rs5388488908:57,079,411C/Auncertain significance
rs21292244968:57,079,616C/Tuncertain significance
rs7488406078:57,079,703C/Tuncertain significance
rs7804348998:57,079,716G/Alikely pathogenic
rs24871072948:57,079,760T/Auncertain significance
rs5747180838:57,079,836G/Tuncertain significance
rs7716902168:57,079,935C/Tuncertain significance
rs2008735078:57,079,946G/Auncertain significance
rs7553906318:57,079,962C/Tuncertain significance
rs773153958:57,080,027T/Alikely benign
rs1498094348:57,080,755C/Tuncertain significance
rs18114148898:57,080,761C/Tuncertain significance
rs1447248638:57,080,762G/Auncertain significance
rs109584768:57,095,808T/Cintron variant
rs78339868:57,100,149G/Aintron variant
rs132731238:57,100,791A/Gintron variant
rs64740518:57,125,270T/Cupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.