PLAT

plasminogen activator, tissue type

Summary

This gene encodes tissue-type plasminogen activator, a secreted serine protease that converts the proenzyme plasminogen to plasmin, a fibrinolytic enzyme. The encoded preproprotein is proteolytically processed by plasmin or trypsin to generate heavy and light chains. These chains associate via disulfide linkages to form the heterodimeric enzyme. This enzyme plays a role in cell migration and tissue remodeling. Increased enzymatic activity causes hyperfibrinolysis, which manifests as excessive bleeding, while decreased activity leads to hypofibrinolysis, which can result in thrombosis or embolism. Alternative splicing of this gene results in multiple transcript variants, at least one of which encodes an isoform that is proteolytically processed. [provided by RefSeq, Jan 2016]

Known Variants56 total

rsidPosition (GRCh37)AllelesClassClinVar
rs18041828:42,033,519G/Abenign
rs7761123958:42,033,567C/Tuncertain significance
rs1411515658:42,033,571C/Tlikely benign
rs9668694918:42,033,572G/Auncertain significance
rs2019672228:42,033,629C/Tlikely benign
rs13209160628:42,033,636C/Tuncertain significance
rs133068248:42,033,661C/Tbenign
rs617554328:42,036,464C/Guncertain significance
rs620018868:42,036,466A/Tlikely benign
rs1145347198:42,036,534A/Glikely benign
rs5649887438:42,036,566G/Auncertain significance
rs10432439568:42,037,459C/Tuncertain significance
rs7569183788:42,037,479T/Guncertain significance
rs2015441568:42,037,483T/Cuncertain significance
rs18051529378:42,037,496C/Guncertain significance
rs7781936448:42,037,506G/Tuncertain significance
rs15879281148:42,037,536C/Auncertain significance
rs5405862828:42,037,541C/Guncertain significance
rs7533205508:42,037,554C/Tlikely benign
rs15879281798:42,037,556G/Alikely benign
rs1498249378:42,037,768T/Cuncertain significance
rs1999606778:42,037,809T/Clikely benign
rs81787818:42,037,815G/Cbenign
rs1485239818:42,037,832C/Guncertain significance
rs1465383358:42,037,851C/Tlikely benign
rs1163816258:42,037,864C/Guncertain significance
rs5470177108:42,037,889G/Tuncertain significance
rs1510069628:42,038,165G/Auncertain significance
rs81787778:42,039,483C/Tbenign
rs1148781478:42,039,484G/Alikely benign
rs1159024608:42,039,506C/Tuncertain significance
rs1147202578:42,039,507G/Abenign
rs3678279518:42,039,518G/Auncertain significance
rs24867579688:42,040,266T/Glikely benign
rs1154755318:42,040,350G/Abenign
rs5564438698:42,042,616G/Tlikely benign
rs413875468:42,042,645C/Glikely benign
rs612315758:42,042,646G/Auncertain significance
rs2011103418:42,042,657G/Alikely benign
rs3741695488:42,042,680G/Cuncertain significance
rs81788858:42,043,637C/Aregulatory region variant
rs630207618:42,043,689T/G
rs7745054108:42,044,950T/Clikely benign
rs1486799568:42,044,964C/Tuncertain significance
rs20209218:42,044,965G/Amissense variant
rs7781502158:42,044,992C/Tuncertain significance
rs5616374688:42,044,993G/Alikely benign
rs1413176688:42,045,020G/Alikely benign
rs1997244238:42,045,030G/Auncertain significance
rs81788848:42,045,041C/Tlikely benign
rs8879654708:42,045,070C/Tuncertain significance
rs7788936328:42,045,469C/Tuncertain significance
rs7572713878:42,046,575C/Tuncertain significance
rs81787338:42,048,904G/Tlikely benign
rs1419646268:42,050,647G/Alikely benign
rs8792938:42,055,146C/Tregulatory region variant

Gene information from NCBI Gene. Variant classifications from ClinVar.