PLEKHN1

pleckstrin homology domain containing N1

Summary

Enables phospholipid binding activity. Involved in 3'-UTR-mediated mRNA destabilization; positive regulation of apoptotic process; and response to hypoxia. Located in several cellular components, including cytoskeleton; cytosol; and mitochondrial membrane. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants89 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1400191961:900,519A/Gmissense variant
rs39350661:900,730G/T
rs626399801:901,922G/Abenign
rs1497411861:901,923C/Abenign
rs13979183071:901,934C/Tuncertain significance
rs1385791151:901,954C/Tuncertain significance
rs3726546251:901,955G/Cuncertain significance
rs1462940161:901,964T/Cuncertain significance
rs7725433311:902,097C/Tuncertain significance
rs7612818631:902,098G/Auncertain significance
rs3716407981:902,104C/Tlikely benign
rs7758718561:902,109G/Auncertain significance
rs7501553661:902,124G/Auncertain significance
rs7463237011:902,160C/Guncertain significance
rs2003797671:902,176C/Tuncertain significance
rs7752991421:905,708A/Cuncertain significance
rs1999822291:905,729C/Tuncertain significance
rs7471724701:905,769A/Guncertain significance
rs412858101:905,894C/Tlikely benign
rs2001915921:905,901G/Auncertain significance
rs9620645711:905,914G/Auncertain significance
rs25229295601:905,922G/Auncertain significance
rs5773343551:905,962C/Guncertain significance
rs3737267481:906,082C/Tlikely benign
rs1442367961:906,100C/Tlikely benign
rs7663803141:906,105G/Cuncertain significance
rs25229343111:906,292C/Guncertain significance
rs1998702721:906,298G/Alikely benign
rs413000901:906,302C/Tlikely benign
rs3732815901:906,303G/Auncertain significance
rs7742088701:906,342G/Auncertain significance
rs3743232291:906,355G/Tuncertain significance
rs5536513541:906,358C/Tlikely benign
rs7778058981:906,360C/Tuncertain significance
rs5528744251:906,363C/Tuncertain significance
rs3708987731:906,364G/Alikely benign
rs25229350661:906,370A/Cuncertain significance
rs5778678531:906,373C/Tuncertain significance
rs7753260011:906,493C/Tuncertain significance
rs7771134391:906,506G/Alikely benign
rs25229379671:906,532C/Tlikely benign
rs11756017751:906,559A/Tuncertain significance
rs25229385651:906,563T/Auncertain significance
rs1464819461:906,758G/Auncertain significance
rs3727880671:907,471G/Auncertain significance
rs7763614481:907,494G/Auncertain significance
rs7575239161:907,513G/Alikely benign
rs7643263351:907,689G/Auncertain significance
rs2011244291:907,691G/Auncertain significance
rs1507114571:907,709G/Auncertain significance
rs1122359401:907,740G/Auncertain significance
rs5769548771:907,784G/Auncertain significance
rs3757043761:908,269C/Tuncertain significance
rs1455745091:908,275G/Abenign
rs7795260831:908,322C/Tuncertain significance
rs9623385181:908,328A/Cuncertain significance
rs7613712391:908,368G/Auncertain significance
rs7670100781:908,370T/Guncertain significance
rs25229609011:908,380A/Guncertain significance
rs13679157991:908,600G/Auncertain significance
rs7478918251:908,602C/Tuncertain significance
rs7602495421:908,611G/Auncertain significance
rs31092151:908,635C/Tuncertain significance
rs5377480091:908,644G/Alikely benign
rs8894323241:908,683C/Tuncertain significance
rs10085730181:908,699T/Guncertain significance
rs1422331121:908,917C/Auncertain significance
rs12881269151:908,919G/Cuncertain significance
rs2012820741:908,944C/Tuncertain significance
rs13490455211:908,958G/Auncertain significance
rs1476712581:908,968C/Tuncertain significance
rs7737779611:908,976G/Auncertain significance
rs561858121:909,222G/Abenign
rs1493190801:909,228C/Guncertain significance
rs726318921:909,247C/Tuncertain significance
rs1454709721:909,253C/Tlikely benign
rs2000943711:909,276G/Tuncertain significance
rs7508315471:909,301G/Auncertain significance
rs2014347201:909,369G/Aconflicting classifications of pathogenicity
rs1492995041:909,406C/Tuncertain significance
rs7507005301:909,715G/Tuncertain significance
rs7563398031:909,718C/Tlikely benign
rs7524610731:909,723G/Auncertain significance
rs7607136291:909,845C/Tuncertain significance
rs7654914961:909,854G/Auncertain significance
rs13797672521:909,897A/Glikely benign
rs7767808631:909,902T/Cuncertain significance
rs3690125841:909,927C/Tuncertain significance
rs5770627421:909,949G/Cuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.