PRKAR1B

protein kinase cAMP-dependent type I regulatory subunit beta

Summary

The protein encoded by this gene is a regulatory subunit of cyclic AMP-dependent protein kinase A (PKA), which is involved in the signaling pathway of the second messenger cAMP. Two regulatory and two catalytic subunits form the PKA holoenzyme, disbands after cAMP binding. The holoenzyme is involved in many cellular events, including ion transport, metabolism, and transcription. Several transcript variants encoding the same protein have been found for this gene. [provided by RefSeq, Aug 2015]

Known Variants83 total

rsidPosition (GRCh37)AllelesClassClinVar
rs21284164437:590,071A/Cuncertain significance
rs24834756277:590,084T/Cuncertain significance
rs7520599397:590,118G/Tlikely benign
rs284889477:590,148G/Abenign
rs1492918197:590,196G/Abenign
rs3746265997:590,198C/Tuncertain significance
rs115450427:590,199A/Gbenign
rs3708298857:590,205C/Tbenign
rs7582400137:590,209C/Tuncertain significance
rs14750003617:590,210G/Apathogenic
rs772709697:590,215C/Tlikely benign
rs286267527:590,229T/Cbenign
rs17841201047:590,244G/Cuncertain significance
rs285859787:590,247T/Gbenign
rs1445663547:591,027G/Alikely benign
rs17841843427:591,056C/Tuncertain significance
rs1480580267:591,062C/Tuncertain significance
rs1444315357:591,063G/Abenign
rs1472200377:591,066C/Tlikely benign
rs8666227527:591,082C/Tlikely pathogenic
rs7487436337:591,085C/Tuncertain significance
rs3759544927:591,086G/Auncertain significance
rs782606517:591,096G/Alikely benign
rs760361137:591,102G/Abenign
rs24834838357:591,104T/Cuncertain significance
rs715183097:591,125G/Cbenign
rs1115120547:617,053G/Aintron variant
rs7576554247:618,886G/Alikely benign
rs32113627:618,938A/Gbenign
rs10149834867:618,940T/Cuncertain significance
rs1996227187:618,965G/Alikely benign
rs778096187:618,974C/Tlikely benign
rs13173643967:618,975G/Auncertain significance
rs17800506107:618,976C/Tuncertain significance
rs12284809247:618,994G/Auncertain significance
rs24831517537:624,186C/Tuncertain significance
rs1868250367:624,211C/Tbenign
rs93303687:624,221T/Gbenign
rs132405637:626,461G/T
rs1472470487:632,002C/Tregulatory region variant
rs284020817:633,179G/C
rs749396127:635,777A/Glikely benign
rs7644472617:635,824G/Cuncertain significance
rs793024547:635,834C/Tbenign
rs760614697:635,849G/Alikely benign
rs13409535627:635,869C/Tuncertain significance
rs763448577:635,905C/Tconflicting classifications of pathogenicity
rs24832437267:635,921C/Tlikely pathogenic
rs3692613197:635,935C/Auncertain significance
rs1456533287:645,842T/Cuncertain significance
rs2012668187:645,851G/Alikely benign
rs14098078317:645,857G/Tuncertain significance
rs7720495097:647,052C/Tuncertain significance
rs285007907:651,147C/A
rs1408919247:664,004G/Aintron variant
rs715183277:664,819C/A
rs1493995067:665,556A/G
rs102338367:669,692A/Gintron variant
rs97713857:672,509G/T
rs754442607:675,581A/Gregulatory region variant
rs1856411797:716,891C/Alikely benign
rs1920662797:720,202G/Alikely benign
rs7574832227:720,246C/Tuncertain significance
rs21285075547:720,267T/Cuncertain significance
rs2004585217:720,274A/Clikely benign
rs5458042737:720,280C/Glikely benign
rs1997996347:720,282G/Cuncertain significance
rs1995688287:720,283G/Tbenign
rs7700202447:720,287G/Cuncertain significance
rs2007494287:720,290G/Auncertain significance
rs2014420777:720,326T/Cuncertain significance
rs12990820477:720,355G/Alikely benign
rs13088129607:720,360C/Tuncertain significance
rs1161985697:720,366G/Abenign
rs7701649347:750,981G/Cuncertain significance
rs10575194907:750,994A/Cuncertain significance
rs617324927:751,025T/Cbenign
rs5303929087:751,042C/Auncertain significance
rs7562320647:751,067C/Tuncertain significance
rs1407356397:751,080G/Alikely benign
rs14574410617:751,090C/Tuncertain significance
rs14337531917:751,142T/Cuncertain significance
rs1153596797:755,987C/A

Gene information from NCBI Gene. Variant classifications from ClinVar.