PRR5

proline rich 5

Summary

This gene encodes a protein with a proline-rich domain. This gene is located in a region of chromosome 22 reported to contain a tumor suppressor gene that may be involved in breast and colorectal tumorigenesis. The protein is a component of the mammalian target of rapamycin complex 2 (mTORC2), and it regulates platelet-derived growth factor (PDGF) receptor beta expression and PDGF signaling to Akt and S6K1. Alternative splicing and the use of alternative promoters results in transcripts encoding different isoforms. Read-through transcripts from this gene into the downstream Rho GTPase activating protein 8 (ARHGAP8) gene also exist, which led to the original description of PRR5 and ARHGAP8 being a single gene. [provided by RefSeq, Nov 2010]

Known Variants31 total

rsidPosition (GRCh37)AllelesClassClinVar
rs192410318122:45,075,719T/Cuncertain significance
rs76533505722:45,075,720C/Tuncertain significance
rs74920791322:45,075,739G/Auncertain significance
rs94911423522:45,075,755G/Tuncertain significance
rs576497222:45,114,177C/Tintron variant
rs600685222:45,115,497G/T
rs2845035822:45,122,513G/Tuncertain significance
rs37176940522:45,127,648T/Guncertain significance
rs20224702122:45,127,649T/Auncertain significance
rs26760626922:45,127,672A/Guncertain significance
rs14245731422:45,128,158G/Auncertain significance
rs118039084722:45,128,191A/Guncertain significance
rs251824564622:45,128,192G/Auncertain significance
rs57240657622:45,128,210C/Tuncertain significance
rs75738533922:45,128,219G/Auncertain significance
rs76029349622:45,128,230C/Tuncertain significance
rs75850384322:45,128,239C/Guncertain significance
rs77433986922:45,128,264T/Cuncertain significance
rs37748182022:45,130,928G/Auncertain significance
rs76346427122:45,132,669C/Tuncertain significance
rs75322931922:45,132,712G/Auncertain significance
rs78022977822:45,132,743C/Guncertain significance
rs77117500822:45,132,762G/Cuncertain significance
rs37332842822:45,132,783G/Auncertain significance
rs5629930522:45,132,831G/Alikely benign
rs77045482222:45,132,864G/Tuncertain significance
rs76531041222:45,132,895C/Tuncertain significance
rs77080788022:45,132,919G/Cuncertain significance
rs75358144922:45,132,969C/Tuncertain significance
rs14109651722:45,132,985G/Alikely benign
rs133913840822:45,132,988C/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.