PXYLP1

2-phosphoxylose phosphatase 1

Summary

Enables phosphatase activity. Involved in chondroitin sulfate proteoglycan biosynthetic process and positive regulation of heparan sulfate proteoglycan biosynthetic process. Located in Golgi apparatus. [provided by Alliance of Genome Resources, Apr 2025]

Known Variants32 total

rsidPosition (GRCh37)AllelesClassClinVar
rs168511913:140,962,198C/Tregulatory region variant
rs3745870803:140,979,061C/Tuncertain significance
rs168512543:140,979,411A/C
rs597522583:140,987,325G/Aregulatory region variant
rs46835913:140,992,260G/Aintron variant
rs1399383753:140,997,262C/Tuncertain significance
rs10401437053:140,998,267C/Tuncertain significance
rs2000149133:140,998,292A/Guncertain significance
rs7750473883:140,998,301C/Tuncertain significance
rs10355706163:140,998,304A/Guncertain significance
rs7541795053:141,006,223G/Auncertain significance
rs15675583:141,008,123A/Gintron variant
rs24731374093:141,011,145A/Tuncertain significance
rs3760856393:141,011,193G/Alikely benign
rs3726384753:141,011,304C/Tuncertain significance
rs7532671213:141,011,317C/Tuncertain significance
rs9814268953:141,011,320T/Cuncertain significance
rs24731396243:141,011,331G/Auncertain significance
rs1467875213:141,011,383G/Auncertain significance
rs1404686343:141,011,398G/Auncertain significance
rs3746750983:141,011,457C/Tuncertain significance
rs12662703243:141,011,496A/Guncertain significance
rs1146444813:141,011,754C/Auncertain significance
rs1429184053:141,011,898A/Guncertain significance
rs7542836693:141,011,919C/Tuncertain significance
rs7576458313:141,011,920A/Tuncertain significance
rs1140617333:141,011,926G/Tuncertain significance
rs7476284733:141,011,947C/Tuncertain significance
rs7465431193:141,011,964C/Tuncertain significance
rs7744175813:141,011,965G/Auncertain significance
rs3730579323:141,012,038A/Tuncertain significance
rs24731470733:141,012,039G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.