RASSF1

Ras association domain family member 1

Summary

This gene encodes a protein similar to the RAS effector proteins. Loss or altered expression of this gene has been associated with the pathogenesis of a variety of cancers, which suggests the tumor suppressor function of this gene. The inactivation of this gene was found to be correlated with the hypermethylation of its CpG-island promoter region. The encoded protein was found to interact with DNA repair protein XPA. The protein was also shown to inhibit the accumulation of cyclin D1, and thus induce cell cycle arrest. Several alternatively spliced transcript variants of this gene encoding distinct isoforms have been reported. [provided by RefSeq, May 2011]

Known Variants24 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1480016133:50,368,030G/Cuncertain significance
rs5877583153:50,368,034A/Guncertain significance
rs5876232333:50,368,055C/Tuncertain significance
rs7821646463:50,368,152C/Tuncertain significance
rs1408051233:50,368,842G/Auncertain significance
rs7579656553:50,368,857C/Guncertain significance
rs558336763:50,368,997G/Abenign
rs2018254023:50,369,010C/Tuncertain significance
rs13768288543:50,369,051G/Cuncertain significance
rs1482221153:50,369,058C/Tuncertain significance
rs7472011233:50,369,073A/Guncertain significance
rs1998962473:50,369,178C/Tuncertain significance
rs7514784173:50,369,184C/Tuncertain significance
rs5877742763:50,369,224C/Tuncertain significance
rs3715879193:50,369,267T/Cbenign
rs785019183:50,369,914A/Gupstream gene variant
rs578387643:50,374,568T/Cregulatory region variant
rs5876783733:50,374,688G/A
rs1499329103:50,374,706G/Alikely benign
rs1931411473:50,376,474A/Tregulatory region variant
rs7668136483:50,378,055G/Cuncertain significance
rs17033354433:50,378,163C/Tuncertain significance
rs3975154603:50,379,478G/Astop gainedpathogenic
rs2009137913:50,379,904A/Gmissense variantpathogenic

Gene information from NCBI Gene. Variant classifications from ClinVar.