RFC2

replication factor C subunit 2

Summary

This gene encodes a member of the activator 1 small subunits family. The elongation of primed DNA templates by DNA polymerase delta and epsilon requires the action of the accessory proteins, proliferating cell nuclear antigen (PCNA) and replication factor C (RFC). Replication factor C, also called activator 1, is a protein complex consisting of five distinct subunits. This gene encodes the 40 kD subunit, which has been shown to be responsible for binding ATP and may help promote cell survival. Disruption of this gene is associated with Williams syndrome. Alternatively spliced transcript variants encoding distinct isoforms have been described. A pseudogene of this gene has been defined on chromosome 2. [provided by RefSeq, Jul 2013]

Known Variants38 total

rsidPosition (GRCh37)AllelesClassClinVar
rs5381536467:73,645,684C/T
rs1396362967:73,646,449G/Alikely benign
rs1493167127:73,646,469C/Tlikely benign
rs7773468467:73,646,521A/Cuncertain significance
rs12304648237:73,646,528T/Cuncertain significance
rs7824827067:73,649,947T/Auncertain significance
rs1483925487:73,651,704G/Alikely benign
rs7820789617:73,651,752T/Glikely benign
rs18053907:73,653,245G/Abenign
rs24874839737:73,653,254T/Auncertain significance
rs31356847:73,653,317G/Alikely benign
rs7818010107:73,654,290G/Auncertain significance
rs1504698287:73,654,315C/Tuncertain significance
rs5482942327:73,654,342C/Tbenign
rs7822937817:73,654,344A/Guncertain significance
rs18053927:73,654,360T/Gbenign
rs11957220377:73,654,375C/Tuncertain significance
rs7825232477:73,654,376G/Alikely benign
rs7818961747:73,654,389G/Auncertain significance
rs7825050487:73,654,396G/Auncertain significance
rs7818261157:73,657,567G/Alikely benign
rs2006294977:73,657,575T/Cuncertain significance
rs12756278247:73,657,584G/Alikely benign
rs1114900067:73,661,039A/Tbenign
rs1999718737:73,661,083C/Tuncertain significance
rs7825840857:73,663,333A/Glikely benign
rs7828077547:73,663,434G/Alikely benign
rs415483127:73,663,451G/Abenign
rs7822569837:73,664,110C/Tuncertain significance
rs1442146087:73,664,114C/Tbenign
rs3751939327:73,666,762T/Clikely benign
rs13639171297:73,668,608G/Alikely benign
rs115380147:73,668,615G/Abenign
rs3766254147:73,668,647C/Alikely benign
rs7825710587:73,668,649G/Auncertain significance
rs7822466967:73,668,667T/Cuncertain significance
rs1508517347:73,668,699G/Tbenign
rs7825103987:73,668,708C/Tlikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.