RILP

Rab interacting lysosomal protein

Summary

This gene encodes a lysosomal protein that interacts with RAB7, a small GTPase that controls transport to endocytic degradative compartments. Studies using mutant forms of the two proteins suggest that this protein represents a downstream effector for RAB7, and both proteins act together in the regulation of late endocytic traffic. A unique region of this protein has also been shown to be involved in the regulation of lysosomal morphology. [provided by RefSeq, Sep 2011]

Known Variants30 total

rsidPosition (GRCh37)AllelesClassClinVar
rs14102499717:1,549,767C/Auncertain significance
rs37497961817:1,549,807C/Tlikely benign
rs74558515817:1,549,822G/Cuncertain significance
rs76025139117:1,549,836C/Auncertain significance
rs191058423217:1,549,848C/Auncertain significance
rs138158361517:1,550,273C/Tuncertain significance
rs75246012617:1,551,181G/Auncertain significance
rs14848658717:1,551,190G/Auncertain significance
rs6173542017:1,551,224G/Asynonymous variant
rs37165118417:1,551,244G/Auncertain significance
rs14539878917:1,551,762G/Cuncertain significance
rs136894377217:1,552,109C/Tuncertain significance
rs74853654217:1,552,113G/Tuncertain significance
rs75648882017:1,552,184C/Tuncertain significance
rs254370208617:1,552,214G/Auncertain significance
rs125181842117:1,552,225C/Guncertain significance
rs87932172617:1,552,265T/Auncertain significance
rs144559367117:1,552,505C/Tuncertain significance
rs76460517617:1,552,558C/Guncertain significance
rs146532046717:1,552,707C/Auncertain significance
rs254370447617:1,552,739G/Auncertain significance
rs254370466017:1,552,790A/Cuncertain significance
rs78024161617:1,552,876C/Guncertain significance
rs77013514617:1,552,887C/Tuncertain significance
rs191086204017:1,552,959C/Tuncertain significance
rs77140378517:1,552,978C/Auncertain significance
rs77481068917:1,552,989G/Auncertain significance
rs20000946217:1,552,993C/Tuncertain significance
rs77511192917:1,553,050C/Tuncertain significance
rs37702819517:1,553,060C/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.