RIMBP2

RIMS binding protein 2

Summary

Predicted to enable voltage-gated calcium channel activity involved in regulation of presynaptic cytosolic calcium levels and voltage-gated monoatomic ion channel activity involved in regulation of presynaptic membrane potential. Predicted to be a structural constituent of presynaptic active zone. Predicted to be involved in neuromuscular synaptic transmission; regulation of calcium-dependent activation of synaptic vesicle fusion; and regulation of presynaptic membrane potential. Predicted to be located in plasma membrane and synapse. Predicted to be active in calyx of Held; glutamatergic synapse; and presynaptic active zone cytoplasmic component. [provided by Alliance of Genome Resources, Jul 2025]

Known Variants75 total

rsidPosition (GRCh37)AllelesClassClinVar
rs254787742612:130,883,697C/Tuncertain significance
rs14601780312:130,884,290T/Guncertain significance
rs75703595212:130,884,331C/Guncertain significance
rs14936279012:130,890,737C/Tuncertain significance
rs77908355512:130,890,761T/Cuncertain significance
rs14467283212:130,890,766C/Guncertain significance
rs74746297512:130,890,778G/Auncertain significance
rs14854255512:130,892,273C/Tuncertain significance
rs15009906412:130,892,350C/Tlikely benign
rs19992815912:130,892,351G/Auncertain significance
rs37293724412:130,898,776G/Auncertain significance
rs55994624112:130,898,834G/Auncertain significance
rs75403240312:130,898,839C/Tuncertain significance
rs14133092812:130,907,000A/Tuncertain significance
rs138839492912:130,908,828C/Tlikely benign
rs98408065512:130,908,906C/Tlikely benign
rs76872988212:130,912,734T/Cuncertain significance
rs76187173912:130,912,743G/Auncertain significance
rs36901792812:130,912,768C/Guncertain significance
rs135425077512:130,912,770T/Cuncertain significance
rs15114917312:130,912,855G/Auncertain significance
rs76699477212:130,912,875C/Tuncertain significance
rs76329786812:130,919,298C/Guncertain significance
rs74542029012:130,919,352T/Cuncertain significance
rs74881791112:130,919,424A/Guncertain significance
rs76817054812:130,921,398C/Guncertain significance
rs77688542012:130,921,421C/Tuncertain significance
rs37122839412:130,921,454G/Tuncertain significance
rs75795449112:130,921,532T/Guncertain significance
rs14181655412:130,921,617C/Tuncertain significance
rs14724517112:130,921,641G/Auncertain significance
rs77455416212:130,921,655G/Auncertain significance
rs13918397612:130,921,668G/Tuncertain significance
rs76262930312:130,921,670G/Tuncertain significance
rs75113896512:130,921,673G/Auncertain significance
rs53074446112:130,921,814G/Auncertain significance
rs14436541012:130,922,956T/Cuncertain significance
rs75306060512:130,923,001C/Tlikely benign
rs20190111412:130,923,034G/Auncertain significance
rs14323781312:130,926,433C/Tlikely benign
rs254819560112:130,926,561A/Glikely benign
rs254819644912:130,926,621G/Tuncertain significance
rs14643533812:130,926,704T/Clikely benign
rs13879349312:130,926,715C/Tlikely benign
rs36869781412:130,926,735C/Tuncertain significance
rs7806792812:130,926,818T/Abenign
rs14197028412:130,926,846C/Tuncertain significance
rs74773242812:130,926,966C/Tuncertain significance
rs13979387112:130,926,979G/Alikely benign
rs98713680412:130,927,001G/Cuncertain significance
rs14842922012:130,927,011C/Tuncertain significance
rs133199102312:130,927,019C/Tuncertain significance
rs77630295912:130,927,038G/Auncertain significance
rs74653396912:130,927,055A/Guncertain significance
rs15097995712:130,927,059G/Auncertain significance
rs14167001012:130,927,074C/Tlikely benign
rs148876075012:130,927,104C/Guncertain significance
rs20089531012:130,927,140C/Tuncertain significance
rs55175064012:130,927,184C/Tuncertain significance
rs14129390012:130,931,580T/Cintron variant
rs19958186312:130,934,746T/Cuncertain significance
rs74557556812:130,934,796G/Auncertain significance
rs37025426612:130,935,763C/Tuncertain significance
rs13911324712:130,935,827C/Alikely benign
rs77813432612:130,935,837C/Tuncertain significance
rs11389522312:130,935,855G/Alikely benign
rs101709618812:130,941,058G/Tuncertain significance
rs254829793612:130,941,109T/Cuncertain significance
rs77695427312:130,941,164G/Auncertain significance
rs37081770212:130,941,214C/Tuncertain significance
rs254841600612:130,963,471C/Auncertain significance
rs37241143812:130,963,523C/Tlikely benign
rs144485093812:130,963,528G/Tuncertain significance
rs146410812:131,022,010A/Cintron variant
rs19237348412:131,097,518C/Tintron variant

Gene information from NCBI Gene. Variant classifications from ClinVar.