RNF111

ring finger protein 111

Summary

The protein encoded by this gene is a nuclear RING-domain containing E3 ubiquitin ligase. This protein interacts with the transforming growth factor (TGF) -beta/NODAL signaling pathway by promoting the ubiquitination and proteosomal degradation of negative regulators, like SMAD proteins, and thereby enhances TGF-beta target-gene transcription. As a modulator of the nodal signaling cascade, this gene plays a critical role in the induction of mesoderm during embryonic development. Alternative splicing of this gene results in multiple transcript variants encoding distinct isoforms. [provided by RefSeq, Jul 2012]

Known Variants61 total

rsidPosition (GRCh37)AllelesClassClinVar
rs77727708115:59,323,044A/Guncertain significance
rs14986991015:59,323,161A/Guncertain significance
rs77983835515:59,323,213C/Auncertain significance
rs147047784315:59,323,368T/Cuncertain significance
rs144835871915:59,323,407A/Cuncertain significance
rs254937414215:59,323,553A/Guncertain significance
rs76903036715:59,323,578G/Auncertain significance
rs14094743315:59,323,592T/Guncertain significance
rs76408423215:59,323,629A/Guncertain significance
rs20144022615:59,323,643C/Tuncertain significance
rs14588207615:59,323,713G/Auncertain significance
rs76784284615:59,323,737G/Auncertain significance
rs75768128915:59,323,752G/Auncertain significance
rs14584261915:59,323,782G/Auncertain significance
rs75086815715:59,323,849T/Guncertain significance
rs19996789115:59,323,865A/Cuncertain significance
rs77225628815:59,344,524G/Tuncertain significance
rs75580741115:59,344,572A/Guncertain significance
rs187456439815:59,344,599G/Auncertain significance
rs137504905615:59,344,608G/Tuncertain significance
rs77984766815:59,344,629C/Tuncertain significance
rs103660321815:59,347,895T/Cuncertain significance
rs20103475815:59,347,945C/Tuncertain significance
rs102020090515:59,347,990C/Auncertain significance
rs254944535515:59,350,560A/Cuncertain significance
rs14229314015:59,350,686T/Alikely benign
rs254944611515:59,350,738C/Tuncertain significance
rs56233737415:59,350,746G/Auncertain significance
rs76067769815:59,358,980A/Glikely benign
rs204267819115:59,359,024G/Tuncertain significance
rs36916627115:59,359,028C/Tuncertain significance
rs14136251115:59,359,079C/Auncertain significance
rs254946793115:59,359,120T/Auncertain significance
rs77786016415:59,359,158C/Tuncertain significance
rs75813000915:59,359,263G/Tuncertain significance
rs204268900115:59,359,268A/Guncertain significance
rs75738277615:59,368,213C/Tuncertain significance
rs20178968415:59,368,261G/Auncertain significance
rs14267835815:59,368,285G/Auncertain significance
rs14743674715:59,368,289C/Tuncertain significance
rs13974251215:59,368,297C/Guncertain significance
rs204315395415:59,368,300A/Guncertain significance
rs74787324315:59,368,307C/Auncertain significance
rs14718955515:59,368,357C/Tuncertain significance
rs76556713415:59,368,370C/Tuncertain significance
rs148896212415:59,368,381C/Tuncertain significance
rs77743585315:59,368,402A/Tuncertain significance
rs75956790315:59,373,194A/Guncertain significance
rs53466512115:59,373,230G/Auncertain significance
rs74796282815:59,373,308C/Tuncertain significance
rs14471004115:59,373,381C/Tuncertain significance
rs75263428915:59,373,396C/Auncertain significance
rs254952195415:59,376,415G/Auncertain significance
rs254952537115:59,377,907G/Auncertain significance
rs77599804315:59,377,937G/Tuncertain significance
rs18118162515:59,377,940C/Tmissense variant
rs37495445515:59,377,957C/Guncertain significance
rs77873487215:59,383,295A/Guncertain significance
rs136377947115:59,384,758A/Guncertain significance
rs207908351815:59,384,802A/Guncertain significance
rs99329611315:59,384,814A/Guncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.