SBDS

SBDS ribosome maturation factor

Summary

This gene encodes a highly conserved protein that plays an essential role in ribosome biogenesis. The encoded protein interacts with elongation factor-like GTPase 1 to disassociate eukaryotic initiation factor 6 from the late cytoplasmic pre-60S ribosomal subunit allowing assembly of the 80S subunit. Mutations within this gene are associated with the autosomal recessive disorder Shwachman-Bodian-Diamond syndrome. This gene has a closely linked pseudogene that is distally located. [provided by RefSeq, Jan 2017]

Known Variants90 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1158548997:66,453,289C/Tbenign
rs1887528057:66,453,375C/Tuncertain significance
rs3777619607:66,453,392T/Cuncertain significance
rs1461668847:66,453,400G/Alikely benign
rs7626485357:66,453,416C/Auncertain significance
rs5434584587:66,453,440A/Guncertain significance
rs7558533147:66,453,445C/Tlikely benign
rs3711330017:66,453,447C/Alikely pathogenic
rs7574972727:66,453,458C/Tconflicting classifications of pathogenicity
rs1139939987:66,453,459G/Astop gainedpathogenic
rs731516757:66,453,460G/Abenign
rs793448187:66,453,476A/Guncertain significance
rs21292312187:66,453,482C/Tlikely pathogenic
rs1139939977:66,456,123C/Tsplice region variantpathogenic
rs25369260497:66,456,135G/Apathogenic
rs14889482867:66,456,169C/Tlikely benign
rs7454851787:66,456,207T/Cuncertain significance
rs5446999947:66,456,224C/Tuncertain significance
rs7749764597:66,456,225G/Amissense variantpathogenic
rs25369261827:66,456,236T/Cuncertain significance
rs1139939967:66,456,243G/Amissense variantpathogenic
rs12264983677:66,456,250C/Guncertain significance
rs13879621587:66,456,270G/Alikely pathogenic
rs17929695827:66,456,289C/Tpathogenic
rs5643264327:66,458,008A/Tbenign
rs1422138357:66,458,112T/Cbenign
rs133117097:66,458,220T/Cuncertain significance
rs25369284147:66,458,232A/Guncertain significance
rs1467804187:66,458,234C/Tlikely benign
rs13760112667:66,458,235G/Alikely pathogenic
rs2010701327:66,458,275C/Tmissense variantpathogenic
rs7666375967:66,458,276G/Alikely benign
rs5357558077:66,458,277G/Cuncertain significance
rs1139939957:66,458,286C/Gmissense variantnot provided
rs1894411067:66,458,306A/Glikely benign
rs7645775617:66,458,312G/Cuncertain significance
rs7580520057:66,458,318C/Tlikely benign
rs3679570347:66,458,330A/Glikely benign
rs21292322697:66,458,337C/Guncertain significance
rs7730594737:66,458,350C/Tuncertain significance
rs11979457577:66,458,389C/Guncertain significance
rs7676956787:66,458,397G/Cuncertain significance
rs15543413637:66,458,403A/Cuncertain significance
rs25369287377:66,458,406T/Glikely pathogenic
rs117632697:66,459,145A/Cbenign
rs5360154967:66,459,151A/Glikely benign
rs1860008477:66,459,180T/Cbenign
rs13418935967:66,459,193A/Guncertain significance
rs1139939937:66,459,197A/Gsplice region variantpathogenic
rs1139939927:66,459,198C/Gpathogenic
rs14738754017:66,459,235C/Alikely benign
rs14582464337:66,459,240T/Guncertain significance
rs10616957:66,459,256T/Cbenign
rs15543414997:66,459,258T/Cuncertain significance
rs1200741607:66,459,273T/Astop gainedpathogenic
rs2003461947:66,459,274A/Glikely benign
rs7472220227:66,459,284A/Guncertain significance
rs15844375927:66,459,290A/Glikely pathogenic
rs3691757787:66,459,293G/Clikely pathogenic
rs1402973267:66,459,297G/Auncertain significance
rs1139939897:66,459,316G/Abenign
rs15543415167:66,459,326T/Cuncertain significance
rs7750572527:66,459,330T/Glikely pathogenic
rs7603640377:66,459,331T/Cconflicting classifications of pathogenicity
rs624665897:66,459,399T/Cbenign
rs5662124597:66,459,404T/Cbenign
rs21292325317:66,459,408A/Gbenign
rs1113315327:66,459,415T/Cbenign
rs3683340497:66,459,488A/Cbenign
rs1136070717:66,459,498C/Tbenign
rs715631477:66,459,513C/Tbenign
rs1114663107:66,459,518T/Gbenign
rs77788817:66,460,011T/Cbenign
rs607124047:66,460,197A/Gbenign
rs25369323157:66,460,274C/Guncertain significance
rs25369323197:66,460,276C/Tlikely pathogenic
rs1476525127:66,460,278C/Aconflicting classifications of pathogenicity
rs10090376787:66,460,297G/Alikely benign
rs5484367327:66,460,298A/Guncertain significance
rs17930805537:66,460,304T/Alikely pathogenic
rs3737308007:66,460,307T/Cmissense variantpathogenic
rs11316918427:66,460,310T/Clikely pathogenic
rs7498306077:66,460,335C/Tuncertain significance
rs15844389087:66,460,344T/Alikely pathogenic
rs7662774887:66,460,364T/Cmissense variantpathogenic
rs7513294847:66,460,365T/Auncertain significance
rs12157365477:66,460,367G/Auncertain significance
rs1458001887:66,460,369T/Clikely benign
rs289420997:66,460,381G/Tmissense variantuncertain significance
rs1829898087:66,460,420A/Tbenign

Gene information from NCBI Gene. Variant classifications from ClinVar.