SCLY

selenocysteine lyase

Summary

Selenocysteine lyase (SCLY; EC 4.4.1.16) catalyzes the pyridoxal 5-prime phosphate-dependent conversion of L-selenocysteine to L-alanine and elemental selenium (Mihara et al., 2000 [PubMed 10692412]).[supplied by OMIM, Mar 2008]

Known Variants54 total

rsidPosition (GRCh37)AllelesClassClinVar
rs12878035982:238,969,690G/Tuncertain significance
rs7684914172:238,969,727C/Tuncertain significance
rs9649089692:238,969,729C/Guncertain significance
rs7719780132:238,973,058G/Tuncertain significance
rs7695298842:238,973,099C/Tlikely benign
rs1418887192:238,976,709G/Tuncertain significance
rs7597263422:238,976,714G/Auncertain significance
rs1388011692:238,976,721A/Guncertain significance
rs7514404372:238,976,738C/Tuncertain significance
rs766257472:238,976,761A/Gbenign
rs7474629942:238,976,763G/Tuncertain significance
rs7799327822:238,976,795G/Auncertain significance
rs1501781922:238,976,802C/Guncertain significance
rs24740948792:238,978,064G/Cuncertain significance
rs24695517602:238,990,364C/Guncertain significance
rs7739622972:238,990,365C/Tuncertain significance
rs7766780062:238,990,400G/Auncertain significance
rs1466675482:238,990,448C/Guncertain significance
rs1152206432:238,990,484C/Tbenign
rs7746615392:238,990,701A/Cuncertain significance
rs7735844172:238,990,708G/Cuncertain significance
rs7655238122:238,990,734G/Auncertain significance
rs3675562532:238,990,761G/Alikely benign
rs7529633332:238,990,797C/Auncertain significance
rs7684786272:238,990,800G/Auncertain significance
rs22787432:238,991,560T/A
rs356373072:238,991,938T/Cbenign
rs1435112492:238,991,979C/Tuncertain significance
rs621959972:238,997,725A/Gintron variant
rs7481424202:238,999,873C/Tuncertain significance
rs1997727752:238,999,875A/Guncertain significance
rs7770797622:239,002,505G/Auncertain significance
rs1394772962:239,002,506C/Guncertain significance
rs7531996662:239,002,526T/Cuncertain significance
rs775538222:239,002,556G/Abenign
rs7557964012:239,002,559C/Tuncertain significance
rs7771175662:239,003,110C/Guncertain significance
rs7622001272:239,003,133A/Cuncertain significance
rs3743304272:239,003,145C/Tuncertain significance
rs5652616782:239,005,489G/Tuncertain significance
rs1390571062:239,005,494G/Clikely benign
rs3697813332:239,005,502C/Tuncertain significance
rs5582919982:239,005,637C/T
rs133951262:239,005,760A/T
rs116820462:239,006,650T/C
rs7753299732:239,006,845C/Tuncertain significance
rs3693572762:239,006,866A/Glikely benign
rs7778019982:239,006,887C/Auncertain significance
rs355441372:239,006,891G/Abenign
rs784755972:239,006,933C/Tbenign
rs7517164022:239,006,934G/Auncertain significance
rs7502030652:239,006,943C/Tuncertain significance
rs1480128542:239,006,974C/Tuncertain significance
rs621960052:239,007,130A/Tregulatory region variant

Gene information from NCBI Gene. Variant classifications from ClinVar.