SELENOO

selenoprotein O

Summary

This gene encodes a selenoprotein that is localized to the mitochondria. It is the largest mammalian selenoprotein, containing the rare amino acid selenocysteine (Sec). Sec is encoded by the UGA codon, which normally signals translation termination. The 3' UTRs of selenoprotein mRNAs contain a conserved stem-loop structure, designated the Sec insertion sequence (SECIS) element, that is necessary for the recognition of UGA as a Sec codon, rather than as a stop signal. The exact function of this selenoprotein is not known, but it is thought to have redox activity. [provided by RefSeq, Dec 2016]

Known Variants87 total

rsidPosition (GRCh37)AllelesClassClinVar
rs100961022:50,638,953A/Ccoding sequence variant
rs57416878622:50,639,470C/Tuncertain significance
rs95438606022:50,639,487C/Guncertain significance
rs137403288022:50,639,490G/Cuncertain significance
rs147274465922:50,639,491G/Auncertain significance
rs126349378522:50,639,550C/Tuncertain significance
rs52812048922:50,639,570C/Glikely benign
rs140790621322:50,639,577A/Guncertain significance
rs206429613022:50,639,593G/Cuncertain significance
rs88995845222:50,639,625G/Tuncertain significance
rs131690875522:50,639,674C/Tuncertain significance
rs121115558922:50,639,728C/Tuncertain significance
rs251909052922:50,639,746G/Auncertain significance
rs137212425022:50,639,765G/Tuncertain significance
rs75399280522:50,639,770C/Tuncertain significance
rs18457581222:50,639,784G/Auncertain significance
rs251909077922:50,639,806G/Auncertain significance
rs89735575422:50,639,810G/Tuncertain significance
rs75057753422:50,639,817G/Tuncertain significance
rs138509618122:50,639,826G/Tuncertain significance
rs75587038522:50,639,841G/Auncertain significance
rs120660158122:50,639,845A/Guncertain significance
rs124253932522:50,639,862G/Tuncertain significance
rs75379333222:50,639,875C/Tuncertain significance
rs138128290422:50,639,906G/Cuncertain significance
rs251909152122:50,639,964A/Glikely benign
rs127730858322:50,639,968G/Auncertain significance
rs119325449922:50,640,015T/Cuncertain significance
rs76925386322:50,644,772G/Auncertain significance
rs20175284822:50,644,783C/Tuncertain significance
rs76388088922:50,644,861T/Guncertain significance
rs136283463322:50,644,862C/Tuncertain significance
rs37709297822:50,644,876G/Auncertain significance
rs20096476222:50,644,879G/Auncertain significance
rs145360224922:50,644,910A/Cuncertain significance
rs76518074222:50,644,921G/Cuncertain significance
rs76569382222:50,647,005A/Guncertain significance
rs20046803022:50,647,012G/Auncertain significance
rs14118080822:50,647,086G/Aconflicting classifications of pathogenicity
rs37524900622:50,647,116G/Auncertain significance
rs78014419822:50,647,141G/Auncertain significance
rs37536366022:50,648,616C/Guncertain significance
rs54362912122:50,648,628C/Tlikely benign
rs36763307122:50,648,629G/Auncertain significance
rs74752532022:50,648,640G/Auncertain significance
rs20164349622:50,648,641A/Guncertain significance
rs76393078022:50,648,670G/Auncertain significance
rs78013352822:50,648,682G/Auncertain significance
rs74987922722:50,648,688A/Guncertain significance
rs77516607622:50,649,070G/Auncertain significance
rs37302491722:50,649,091G/Auncertain significance
rs74930271822:50,649,100G/Auncertain significance
rs18777473122:50,649,103C/Tuncertain significance
rs75080861922:50,649,127G/Auncertain significance
rs37087400522:50,649,160G/Auncertain significance
rs20013843222:50,649,223G/Cuncertain significance
rs5637299122:50,649,273C/Tsynonymous variant
rs20093905622:50,649,274G/Auncertain significance
rs14361774922:50,652,678C/Tdownstream gene variant
rs92106988622:50,654,239A/Guncertain significance
rs54758995222:50,655,170C/Tuncertain significance
rs55484234522:50,655,212G/Auncertain significance
rs77870523422:50,655,224A/Guncertain significance
rs53703785222:50,655,248C/Tuncertain significance
rs37105520322:50,655,253G/Cuncertain significance
rs76811176022:50,655,299C/Tuncertain significance
rs76082649422:50,655,406G/Auncertain significance
rs3465800422:50,655,416G/Cuncertain significance
rs57014120322:50,655,429G/Auncertain significance
rs36975005222:50,655,444G/Auncertain significance
rs77686883122:50,655,459C/Guncertain significance
rs54850770322:50,655,465C/Tuncertain significance
rs37653122122:50,655,466G/Auncertain significance
rs20086855022:50,655,468G/Auncertain significance
rs57081215722:50,655,477G/Auncertain significance
rs75880854122:50,655,480A/Guncertain significance
rs75197399622:50,655,525A/Tuncertain significance
rs77795671122:50,655,536C/Tlikely benign
rs77200115822:50,655,540C/Tuncertain significance
rs77611871322:50,655,546G/Cuncertain significance
rs251911613422:50,655,634G/Auncertain significance
rs78078022822:50,655,641G/Auncertain significance
rs37485655022:50,655,672C/Guncertain significance
rs37255095922:50,655,707C/Tuncertain significance
rs76062213122:50,655,742T/Cuncertain significance
rs77801949522:50,655,778T/Cuncertain significance
rs38790701922:50,656,167A/Cstop lostpathogenic

Gene information from NCBI Gene. Variant classifications from ClinVar.