SETDB1

SET domain bifurcated histone lysine methyltransferase 1

Summary

This gene encodes a histone methyltransferase which regulates histone methylation, gene silencing, and transcriptional repression. This gene has been identified as a target for treatment in Huntington Disease, given that gene silencing and transcription dysfunction likely play a role in the disease pathogenesis. Alternatively spliced transcript variants of this gene have been described.[provided by RefSeq, Jun 2011]

Known Variants39 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1397558561:150,899,588C/Tintron variant
rs1388784301:150,902,440T/Clikely benign
rs7630988711:150,902,497A/Glikely benign
rs28672961:150,903,234G/Cintron variant
rs65875421:150,907,701G/C
rs716245141:150,911,352C/Tintron variant
rs1932788011:150,912,407C/Tlikely benign
rs2009453231:150,912,430A/Clikely benign
rs3742396681:150,912,453A/Glikely benign
rs7613316711:150,913,843A/Cuncertain significance
rs3675809191:150,915,043C/Tlikely benign
rs7556463751:150,915,142C/Glikely benign
rs15580171161:150,915,326A/Guncertain significance
rs1425333941:150,915,377A/Glikely benign
rs25278891141:150,915,433T/Cuncertain significance
rs5875945501:150,916,466C/Guncertain significance
rs7694848581:150,917,404T/Clikely benign
rs25279172401:150,919,459A/Guncertain significance
rs11844804241:150,919,483A/Guncertain significance
rs66949781:150,919,842C/Tintron variant
rs1146239951:150,921,669C/Tlikely benign
rs1132960721:150,921,737C/Gbenign
rs1432249121:150,922,939C/Tlikely benign
rs25279381261:150,923,182G/Auncertain significance
rs7782690331:150,923,574G/Clikely benign
rs7500278501:150,923,892A/Glikely benign
rs15716509321:150,923,898C/Glikely benign
rs25279909631:150,933,230C/Guncertain significance
rs16707954771:150,933,359G/Cuncertain significance
rs1478629341:150,933,394T/Clikely benign
rs1131109911:150,933,468C/Tlikely benign
rs1508926411:150,933,600C/Tbenign
rs2006017321:150,935,152A/Guncertain significance
rs757438571:150,935,173C/Tbenign
rs1458308651:150,935,539G/Alikely benign
rs7553832711:150,935,605G/Tuncertain significance
rs25280129821:150,936,054T/Guncertain significance
rs16709103171:150,936,481G/Auncertain significance
rs1497821271:150,936,738G/Tbenign

Gene information from NCBI Gene. Variant classifications from ClinVar.