SETMAR

SET and mariner transposase domain methyltransferase

Summary

This gene encodes a fusion protein that contains an N-terminal histone-lysine N-methyltransferase domain and a C-terminal mariner transposase domain. The encoded protein binds DNA and functions in DNA repair activities including non-homologous end joining and double strand break repair. The SET domain portion of this protein specifically methylates histone H3 lysines 4 and 36. This gene exists as a fusion gene only in anthropoid primates, other organisms lack mariner transposase domain. Alternate splicing results in multiple transcript variants. [provided by RefSeq, Jan 2013]

Known Variants30 total

rsidPosition (GRCh37)AllelesClassClinVar
rs24704749453:4,345,077C/Guncertain significance
rs7628533753:4,345,082C/Tuncertain significance
rs7563229433:4,345,097G/Auncertain significance
rs16980317913:4,345,121G/Auncertain significance
rs24704768813:4,345,169G/Auncertain significance
rs24704768963:4,345,170T/Guncertain significance
rs9708834163:4,345,178T/Guncertain significance
rs24704776163:4,345,205T/Guncertain significance
rs1905408913:4,345,338G/Tregulatory region variant
rs2012336673:4,354,617C/Guncertain significance
rs5388955663:4,354,645G/Auncertain significance
rs7699305593:4,354,664C/Tuncertain significance
rs7791899773:4,354,858A/Guncertain significance
rs7773389153:4,354,885C/Tuncertain significance
rs7591358783:4,354,904C/Tuncertain significance
rs10020822893:4,354,922G/Cuncertain significance
rs13163260563:4,354,958T/Cuncertain significance
rs1499441423:4,355,132G/Auncertain significance
rs7543474073:4,355,167G/Auncertain significance
rs7809426343:4,355,188G/Auncertain significance
rs1476605453:4,355,264A/Tuncertain significance
rs1424494703:4,355,265T/Clikely benign
rs24705541823:4,355,267G/Auncertain significance
rs7721963553:4,355,324T/Alikely benign
rs1411942093:4,355,347G/Auncertain significance
rs24705556543:4,355,392A/Cuncertain significance
rs1447005713:4,355,434T/Auncertain significance
rs24705561223:4,355,437A/Guncertain significance
rs1471843303:4,358,102A/Glikely benign
rs1496118903:4,358,138C/Tlikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.