SH3BP1

SH3 domain binding protein 1

Summary

This gene encodes a member of the Rho GTPase activating protein (RhoGAP) family. The encoded protein regulates Rac signaling and plays a role in cytoskeletal dynamics, cell motility and epithelial junction formation. This protein's association with the exocyst complex, which tethers secretory vesicles to the plasma membrane, has been demonstrated to be important in cell motility. In a distinct complex, this protein has been shown to regulate epithelial junction formation and morphogenesis. By interacting with the Plexin-D1 cell surface receptor, this protein mediates changes in the cytoskeleton in response to semaphorin binding. This protein may promote metastasis in human liver cancer cells and tissues. [provided by RefSeq, Mar 2017]

Known Variants52 total

rsidPosition (GRCh37)AllelesClassClinVar
rs251806888222:38,035,837A/Tuncertain significance
rs76783984522:38,037,146G/Auncertain significance
rs20125377722:38,037,158G/Auncertain significance
rs11468639122:38,037,374T/Cbenign
rs91308275422:38,037,391G/Auncertain significance
rs7464319222:38,037,401G/Abenign
rs122556278122:38,037,432C/Tuncertain significance
rs76669936122:38,037,453G/Tuncertain significance
rs37202282422:38,037,465G/Cuncertain significance
rs193259563922:38,037,478A/Guncertain significance
rs130802023922:38,037,480C/Tuncertain significance
rs136552527722:38,038,979G/Auncertain significance
rs74836137822:38,038,993C/Guncertain significance
rs91511172522:38,039,704C/Tuncertain significance
rs37134667822:38,040,931G/Tuncertain significance
rs74952583522:38,041,389A/Glikely benign
rs251808294722:38,041,390C/Tuncertain significance
rs53821514522:38,041,443G/Auncertain significance
rs53835786422:38,041,453G/Auncertain significance
rs103001880022:38,041,473G/Auncertain significance
rs77782200922:38,041,482G/Auncertain significance
rs14488858522:38,042,886C/Tuncertain significance
rs76378383522:38,043,464G/Cuncertain significance
rs75129031422:38,043,468G/Auncertain significance
rs74534457022:38,043,506C/Guncertain significance
rs75559107322:38,043,507C/Guncertain significance
rs36964698222:38,043,511G/Alikely benign
rs14666464822:38,046,173T/Guncertain significance
rs76465594722:38,046,188T/Cuncertain significance
rs7342275522:38,046,235G/Tuncertain significance
rs76260251722:38,046,242C/Guncertain significance
rs14146274922:38,046,644G/Auncertain significance
rs77577221922:38,046,645T/Cuncertain significance
rs961082522:38,048,755C/Tintron variant
rs76088994922:38,049,777C/Tlikely benign
rs77112570222:38,049,793T/Cuncertain significance
rs75681780622:38,049,837T/Auncertain significance
rs76989448122:38,051,285G/Auncertain significance
rs76834909522:38,051,288C/Auncertain significance
rs76591260922:38,051,300G/Auncertain significance
rs75766821422:38,051,315C/Guncertain significance
rs78161593922:38,051,317C/Tuncertain significance
rs251810368022:38,051,327C/Tuncertain significance
rs140233453522:38,051,351C/Auncertain significance
rs11367558622:38,051,361G/Cuncertain significance
rs129455730122:38,051,479C/Tuncertain significance
rs77506593022:38,051,480G/Auncertain significance
rs76234371322:38,051,482C/Tuncertain significance
rs76801652522:38,051,483G/Auncertain significance
rs75075842222:38,051,486A/Guncertain significance
rs78078472422:38,051,650C/Tuncertain significance
rs37741729022:38,051,668A/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.