SHQ1

SHQ1, H/ACA ribonucleoprotein assembly factor

Summary

SHQ1 assists in the assembly of H/ACA-box ribonucleoproteins that function in the processing of ribosomal RNAs, modification of spliceosomal small nuclear RNAs, and stabilization of telomerase (see MIM 602322) (Grozdanov et al., 2009 [PubMed 19383767]).[supplied by OMIM, Dec 2010]

Known Variants53 total

rsidPosition (GRCh37)AllelesClassClinVar
rs98807633:72,789,805G/Cintergenic variant
rs1444983513:72,799,481C/Tlikely benign
rs5710509073:72,799,482G/Auncertain significance
rs1996561633:72,799,494T/Guncertain significance
rs340319573:72,799,548C/Tbenign
rs24715674243:72,799,556A/Cuncertain significance
rs10477310473:72,799,589G/Auncertain significance
rs1451508773:72,799,641G/Alikely benign
rs11578067493:72,799,686A/Cuncertain significance
rs7455844233:72,799,691C/Auncertain significance
rs13098434003:72,799,707C/Auncertain significance
rs5417675973:72,799,773A/Guncertain significance
rs7795902423:72,799,799G/Auncertain significance
rs13070310183:72,799,935T/Cuncertain significance
rs12650282593:72,799,943G/Cuncertain significance
rs98149453:72,803,590C/A
rs1451735383:72,806,191G/Tregulatory region variant
rs119227943:72,813,582G/Cintron variant
rs24716181893:72,842,133T/Cuncertain significance
rs760524643:72,861,831A/Gbenign
rs7595319643:72,861,885G/Cconflicting classifications of pathogenicity
rs7557870433:72,861,948G/Cuncertain significance
rs14207546463:72,866,389C/Tuncertain significance
rs15596869223:72,866,412T/Cuncertain significance
rs17073466493:72,866,430A/Gconflicting classifications of pathogenicity
rs13758555613:72,873,598T/Cuncertain significance
rs1413484983:72,873,658T/Cuncertain significance
rs1458411893:72,873,677T/Clikely benign
rs3757641923:72,873,694A/Cuncertain significance
rs7793105993:72,881,532G/Tuncertain significance
rs7460768793:72,881,562C/Tuncertain significance
rs1436369683:72,881,596C/Aconflicting classifications of pathogenicity
rs788644163:72,881,614T/Cbenign
rs7531255723:72,881,617C/Tuncertain significance
rs7649500553:72,890,204G/Auncertain significance
rs7803335353:72,890,239T/Cuncertain significance
rs617340403:72,890,281C/Tbenign
rs1437705213:72,891,500G/Abenign
rs7654051533:72,891,521G/Cuncertain significance
rs784916063:72,891,547A/Cmissense variant
rs13810887783:72,893,539C/Tuncertain significance
rs17082687083:72,893,543C/Tuncertain significance
rs7620606843:72,893,574T/Clikely benign
rs7602211653:72,897,402G/Tuncertain significance
rs1480305883:72,897,412G/Auncertain significance
rs3757226953:72,897,421G/Tuncertain significance
rs24712926863:72,897,437T/Cuncertain significance
rs7699980673:72,897,455C/Guncertain significance
rs7590930413:72,897,458G/Auncertain significance
rs1462201823:72,897,459A/Clikely benign
rs24712929023:72,897,463T/Cuncertain significance
rs795348353:72,897,467T/Cbenign
rs24712929653:72,897,470G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.