SIGLEC8

sialic acid binding Ig like lectin 8

Summary

Sialic acid-binding immunoglobulin (Ig)-like lectins, or SIGLECs (e.g., CD33 (MIM 159590)), are a family of type 1 transmembrane proteins each having a unique expression pattern, mostly in hemopoietic cells. SIGLEC8 is a member of the CD33-like subgroup of SIGLECs, which are localized to 19q13.3-q13.4 and have 2 conserved cytoplasmic tyrosine-based motifs: an immunoreceptor tyrosine-based inhibitory motif, or ITIM (see MIM 604964), and a motif homologous to one identified in signaling lymphocyte activation molecule (SLAM; MIM 603492) that mediates an association with SLAM-associated protein (SAP; MIM 300490) (summarized by Foussias et al., 2000 [PubMed 11095983]).[supplied by OMIM, May 2010]

Known Variants38 total

rsidPosition (GRCh37)AllelesClassClinVar
rs74708937819:51,955,700C/Tuncertain significance
rs171853768019:51,955,742T/Guncertain significance
rs251390237919:51,955,812C/Tuncertain significance
rs11480940919:51,955,840A/Cbenign
rs56684170919:51,957,496C/Tuncertain significance
rs14476929319:51,957,987C/Tuncertain significance
rs37565599319:51,958,674G/Auncertain significance
rs251390768519:51,958,731T/Cuncertain significance
rs13870063119:51,958,737C/Tlikely benign
rs77534988419:51,958,743G/Auncertain significance
rs37397060719:51,958,765C/Tuncertain significance
rs77931642119:51,958,833C/Guncertain significance
rs251390797019:51,958,857G/Tuncertain significance
rs77632568219:51,958,858G/Auncertain significance
rs76941691819:51,958,867T/Clikely benign
rs74692908219:51,958,922A/Tuncertain significance
rs14944461019:51,960,717G/Abenign
rs36878443019:51,960,733C/Tlikely benign
rs53115144519:51,960,745T/Cuncertain significance
rs75126641919:51,960,822A/Guncertain significance
rs36823885719:51,960,835G/Auncertain significance
rs14095825819:51,960,873A/Guncertain significance
rs128846582419:51,960,877A/Guncertain significance
rs198953001619:51,960,909G/Tuncertain significance
rs1040996219:51,960,940A/Gmissense variant
rs76137296119:51,961,223T/Cuncertain significance
rs6173519819:51,961,257C/Guncertain significance
rs18672110319:51,961,268C/Tuncertain significance
rs123556259719:51,961,301G/Auncertain significance
rs121786216719:51,961,333C/Auncertain significance
rs6173519919:51,961,358C/Tmissense variant
rs20117885119:51,961,406A/Guncertain significance
rs78009830619:51,961,439C/Tuncertain significance
rs76844566119:51,961,446A/Guncertain significance
rs6173520119:51,961,504G/Abenign
rs76930526919:51,961,565C/Tuncertain significance
rs77047710919:51,961,604C/Tuncertain significance
rs14866054719:51,963,490A/Gupstream gene variant

Gene information from NCBI Gene. Variant classifications from ClinVar.