SIPA1L3

signal induced proliferation associated 1 like 3

Summary

This gene belongs to the signal induced proliferation associated 1 family of genes, which encode GTPase-activating proteins specific for the GTP-binding protein Rap1. Rap1 has been implicated in regulation of cell adhesion, cell polarity, and organization of the cytoskeleton. Like other members of the family, the protein encoded by this gene contains RapGAP and PDZ domains. In addition, this protein contains a C-terminal leucine zipper domain. This gene is proposed to function in epithelial cell morphogenesis and establishment or maintenance of polarity. Consistently, expression of the protein in cell culture showed localization to cell-cell borders in apical regions, and downregulation of the gene in 3D Caco2 cell culture resulted in abnormal cell polarity and morphogenesis. Allelic variants of this gene have been associated with congenital cataracts in humans. [provided by RefSeq, Feb 2016]

Known Variants337 total

rsidPosition (GRCh37)AllelesClassClinVar
rs5624644619:38,404,660G/T
rs35341119:38,442,897G/Cintron variant
rs7303493519:38,458,414T/A
rs14833012219:38,520,324C/Tintron variant
rs172551219:38,571,728A/Gbenign
rs122384325919:38,572,209A/Guncertain significance
rs251363386219:38,572,239G/Auncertain significance
rs99466993119:38,572,243A/Guncertain significance
rs76564100419:38,572,263G/Auncertain significance
rs14720827119:38,572,275G/Auncertain significance
rs14867523719:38,572,280C/Tbenign
rs74613905219:38,572,281C/Tuncertain significance
rs251363400819:38,572,285C/Guncertain significance
rs11224231919:38,572,304C/Glikely benign
rs77165256719:38,572,333A/Cuncertain significance
rs76436144119:38,572,373C/Glikely benign
rs160002805019:38,572,377A/Cuncertain significance
rs77202125319:38,572,401C/Auncertain significance
rs74653336419:38,572,418T/Alikely benign
rs77633134019:38,572,421C/Tlikely benign
rs122718770319:38,572,471A/Guncertain significance
rs77914750019:38,572,474G/Auncertain significance
rs14098266519:38,572,533G/Auncertain significance
rs7363082719:38,572,546C/Abenign
rs14678763019:38,572,571C/Tlikely benign
rs20090691419:38,572,597C/Tbenign
rs251363552719:38,572,612A/Glikely benign
rs14046683319:38,572,614G/Auncertain significance
rs75254285119:38,572,615C/Tuncertain significance
rs37692166919:38,572,624G/Cuncertain significance
rs196999590819:38,572,633G/Auncertain significance
rs13847631119:38,572,647G/Tuncertain significance
rs76535332719:38,572,650G/Cuncertain significance
rs76425163319:38,572,665G/Auncertain significance
rs20176602119:38,572,678C/Tuncertain significance
rs14919896419:38,572,706G/Clikely benign
rs251363595719:38,572,723A/Cuncertain significance
rs20160196719:38,572,747C/Tconflicting classifications of pathogenicity
rs118624087719:38,572,758G/Auncertain significance
rs14834169919:38,572,774C/Glikely benign
rs18475150219:38,572,777G/Abenign
rs78059534219:38,572,833G/Auncertain significance
rs146510967419:38,572,834T/Cuncertain significance
rs105688186519:38,572,847C/Glikely benign
rs14736660919:38,572,881C/Tuncertain significance
rs6172913619:38,572,882G/Auncertain significance
rs251363673219:38,572,885G/Tuncertain significance
rs4557294019:38,572,894T/Cbenign
rs77935406519:38,572,912A/Guncertain significance
rs75936058519:38,572,954T/Auncertain significance
rs124618332819:38,572,956A/Tuncertain significance
rs118773304619:38,572,980G/Cuncertain significance
rs197001166919:38,572,984A/Tuncertain significance
rs76710996419:38,572,987C/Tuncertain significance
rs20084144819:38,572,993A/Glikely benign
rs37527688819:38,573,025C/Guncertain significance
rs37207877719:38,573,036G/Abenign
rs14195872819:38,573,053C/Tlikely benign
rs15067454619:38,573,068C/Tlikely benign
rs75881169819:38,573,076C/Tuncertain significance
rs197001647219:38,573,080G/Auncertain significance
rs36768911119:38,573,096G/Alikely benign
rs56865977619:38,573,112C/Guncertain significance
rs76029202619:38,573,124A/Cuncertain significance
rs6212143019:38,573,139T/Gbenign
rs1040566719:38,573,149G/Cbenign
rs76767296119:38,573,152G/Auncertain significance
rs13961212719:38,573,158C/Tlikely benign
rs92668374519:38,573,179G/Auncertain significance
rs251363817619:38,573,191A/Cuncertain significance
rs14972864619:38,573,204G/Alikely benign
rs13986593019:38,573,210G/Abenign
rs14681214119:38,573,267G/Clikely benign
rs78077202419:38,573,269C/Tuncertain significance
rs76222716419:38,573,286T/Cuncertain significance
rs100784146319:38,573,296A/Cuncertain significance
rs36908839419:38,573,298C/Tuncertain significance
rs37328395319:38,573,310A/Tuncertain significance
rs6172913219:38,573,333C/Tbenign
rs77366015519:38,573,334G/Auncertain significance
rs6172913319:38,573,347C/Tbenign
rs6172913419:38,573,357C/Gbenign
rs6172913519:38,573,366G/Abenign
rs37143934919:38,573,382G/Auncertain significance
rs13800920219:38,573,385G/Auncertain significance
rs94245467519:38,573,404C/Tuncertain significance
rs13952524619:38,573,450C/Tbenign
rs76892686419:38,573,514G/Auncertain significance
rs18876540119:38,573,518G/Auncertain significance
rs19958527319:38,573,544G/Cuncertain significance
rs77316653519:38,573,571G/Auncertain significance
rs14137347019:38,573,620G/Alikely benign
rs100477952119:38,573,656G/Auncertain significance
rs251364005019:38,573,672C/Glikely benign
rs156897519:38,573,802T/Cbenign
rs5629354719:38,574,772G/A
rs85563819:38,579,285T/Cbenign
rs13840231019:38,579,450G/Auncertain significance
rs14310008119:38,579,496G/Clikely benign
rs19161899319:38,579,510G/Abenign

Showing 100 of 337 variants. Use the SNP search for the full list.

Gene information from NCBI Gene. Variant classifications from ClinVar.