SKP2

S-phase kinase associated protein 2

Summary

This gene encodes a member of the F-box protein family which is characterized by an approximately 40 amino acid motif, the F-box. The F-box proteins constitute one of the four subunits of ubiquitin protein ligase complex called SCFs (SKP1-cullin-F-box), which function in phosphorylation-dependent ubiquitination. The F-box proteins are divided into 3 classes: Fbws containing WD-40 domains, Fbls containing leucine-rich repeats, and Fbxs containing either different protein-protein interaction modules or no recognizable motifs. The protein encoded by this gene belongs to the Fbls class; in addition to an F-box, this protein contains 10 tandem leucine-rich repeats. This protein is an essential element of the cyclin A-CDK2 S-phase kinase. It specifically recognizes phosphorylated cyclin-dependent kinase inhibitor 1B (CDKN1B, also referred to as p27 or KIP1) predominantly in S phase and interacts with S-phase kinase-associated protein 1 (SKP1 or p19). In addition, this gene is established as a protooncogene causally involved in the pathogenesis of lymphomas. Alternative splicing of this gene generates three transcript variants encoding different isoforms. [provided by RefSeq, Jul 2011]

Known Variants14 total

rsidPosition (GRCh37)AllelesClassClinVar
rs1835193115:36,151,557C/Aupstream gene variant
rs7746660995:36,152,941C/Tuncertain significance
rs23629745:36,156,654G/Aregulatory region variant
rs7505561055:36,168,422C/Tuncertain significance
rs25461308275:36,170,499G/Tuncertain significance
rs169027805:36,175,787A/Gintron variant
rs25461382005:36,177,304A/Cuncertain significance
rs424255:36,178,293C/Tregulatory region variant
rs25461433065:36,181,934T/Cuncertain significance
rs11615681265:36,181,990C/Guncertain significance
rs25461436225:36,182,124T/Auncertain significance
rs25461436365:36,182,129T/Auncertain significance
rs2018442975:36,183,958G/Auncertain significance
rs1405241035:36,184,072G/Tuncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.