SPIRE1

spire type actin nucleation factor 1

Summary

Spire proteins, such as SPIRE1, are highly conserved between species. They belong to the family of Wiskott-Aldrich homology region-2 (WH2) proteins, which are involved in actin organization (Kerkhoff et al., 2001 [PubMed 11747823]).[supplied by OMIM, Mar 2008]

Known Variants43 total

rsidPosition (GRCh37)AllelesClassClinVar
rs76180632318:12,449,653G/Tuncertain significance
rs74865600918:12,449,684C/Guncertain significance
rs37604149418:12,449,696T/Clikely benign
rs75215967918:12,449,761C/Tuncertain significance
rs37734256518:12,452,263C/Auncertain significance
rs76787057618:12,452,275C/Tuncertain significance
rs75612445518:12,452,279G/Auncertain significance
rs251021940118:12,452,288T/Guncertain significance
rs126311709318:12,452,318C/Guncertain significance
rs76942062818:12,452,354T/Cuncertain significance
rs251022400518:12,454,364G/Auncertain significance
rs14862767518:12,454,384T/Auncertain significance
rs36839912718:12,463,394C/Tuncertain significance
rs14128645518:12,463,405G/Auncertain significance
rs53629685318:12,463,484T/Cuncertain significance
rs36808783818:12,464,876T/Auncertain significance
rs251024340718:12,464,879A/Tuncertain significance
rs75826245018:12,479,730T/Cuncertain significance
rs203302351218:12,485,961A/Guncertain significance
rs75042188918:12,485,993C/Tuncertain significance
rs57437770218:12,491,960C/A
rs75956798818:12,493,083G/Auncertain significance
rs251029602018:12,493,125C/Tuncertain significance
rs14064776518:12,506,573C/Tuncertain significance
rs1166339118:12,516,768C/Aintron variant
rs77056390818:12,546,263C/T
rs3493361118:12,546,603G/A
rs15008567418:12,546,695C/Tuncertain significance
rs14823967218:12,546,778A/Glikely benign
rs75452202418:12,546,899A/Guncertain significance
rs194097318:12,550,747T/Cintron variant
rs995914518:12,606,463G/A
rs103034325918:12,657,552G/Cuncertain significance
rs203858659818:12,657,558T/Guncertain significance
rs75324795918:12,657,626G/Cuncertain significance
rs76483830418:12,657,644G/Alikely benign
rs91012595418:12,657,663G/Auncertain significance
rs203859139718:12,657,664A/Cuncertain significance
rs132670289318:12,657,666C/Tuncertain significance
rs116615605118:12,657,753T/Cuncertain significance
rs134504238218:12,657,787C/Guncertain significance
rs144396732718:12,657,795C/Tuncertain significance
rs57795452218:12,657,855G/Auncertain significance

Gene information from NCBI Gene. Variant classifications from ClinVar.