SSH1

slingshot protein phosphatase 1

Summary

The protein encoded by this gene belongs to the slingshot homolog (SSH) family of phosphatases, which regulate actin filament dynamics. The SSH proteins dephosphorylate and activate the actin binding/depolymerizing factor cofilin, which subsequently binds to actin filaments and stimulates their disassembly. Cofilin is inactivated by kinases such as LIM domain kinase-1 (LIMK1), which may also be dephosphorylated and inactivated by SSH proteins. The SSH family thus appears to play a role in actin dynamics by reactivating cofilin proteins. Alternatively spliced transcript variants encoding different isoforms have been described for this gene. [provided by RefSeq, Aug 2011]

Known Variants73 total

rsidPosition (GRCh37)AllelesClassClinVar
rs19008843712:109,179,282C/G
rs249979483112:109,181,800T/Guncertain significance
rs75614150512:109,181,891G/Auncertain significance
rs6173930212:109,181,932A/Cconflicting classifications of pathogenicity
rs74613129212:109,182,081G/Auncertain significance
rs79650944412:109,182,144T/Auncertain significance
rs132303457612:109,182,147G/Auncertain significance
rs145787676312:109,182,158A/Guncertain significance
rs18558167312:109,182,198C/Tuncertain significance
rs102951430812:109,182,203C/Tuncertain significance
rs78034155412:109,182,257G/Tuncertain significance
rs19007101612:109,182,258C/Tuncertain significance
rs36762083812:109,182,282C/Tuncertain significance
rs77861032412:109,182,317T/Guncertain significance
rs13875972712:109,182,356G/Auncertain significance
rs74977369412:109,182,395G/Cuncertain significance
rs77419191512:109,182,645A/Cuncertain significance
rs15117641012:109,182,653G/Alikely benign
rs14131755412:109,182,672G/Auncertain significance
rs6173930512:109,182,771G/Cbenign
rs77092379812:109,182,776G/Alikely benign
rs103802913612:109,182,797G/Cuncertain significance
rs76472849412:109,182,805C/Guncertain significance
rs76348978912:109,182,812G/Alikely benign
rs75192697512:109,182,818C/Tuncertain significance
rs78165068712:109,182,824C/Tuncertain significance
rs11690314412:109,182,881G/Alikely benign
rs14893688712:109,182,891C/Tuncertain significance
rs14370260512:109,182,899T/Clikely benign
rs249981556212:109,182,920C/Tuncertain significance
rs77049731612:109,186,073T/Clikely benign
rs74753485612:109,186,111G/Auncertain significance
rs20108264312:109,186,130C/Guncertain significance
rs159300747712:109,186,154A/Cuncertain significance
rs37455238712:109,186,187T/Cuncertain significance
rs54082993012:109,186,217G/Auncertain significance
rs75176016612:109,186,225G/Auncertain significance
rs140169902112:109,186,414A/Tuncertain significance
rs14445012112:109,186,436G/Cuncertain significance
rs37138226912:109,186,460C/Tlikely benign
rs14793614712:109,186,501T/Alikely benign
rs14514188412:109,186,505G/Alikely benign
rs56217570712:109,192,836G/Auncertain significance
rs76741947712:109,192,936C/Auncertain significance
rs75641303612:109,194,596C/Tuncertain significance
rs14015100812:109,198,832G/Abenign
rs86812698212:109,198,889C/Guncertain significance
rs203721208112:109,198,957G/Auncertain significance
rs37707749112:109,200,144C/Tuncertain significance
rs54686357312:109,200,148C/Tuncertain significance
rs54927544112:109,201,261G/A
rs77905857012:109,201,437G/Tuncertain significance
rs203735503012:109,201,457T/Cuncertain significance
rs115727386312:109,201,511T/Cuncertain significance
rs77437910312:109,201,543G/Alikely benign
rs13949726912:109,201,562C/Tuncertain significance
rs118401810312:109,201,572C/Tuncertain significance
rs126938287612:109,203,530A/Cuncertain significance
rs203792258912:109,210,868C/Tuncertain significance
rs77134769012:109,210,910G/Auncertain significance
rs11447459412:109,210,929G/Abenign
rs250018333912:109,217,043T/Cuncertain significance
rs78085029612:109,217,076G/Auncertain significance
rs14289669212:109,217,101G/Abenign
rs11293464612:109,222,130A/G
rs14519805712:109,246,411T/Alikely benign
rs19994777612:109,246,419G/Cuncertain significance
rs78174021612:109,246,430G/Cuncertain significance
rs203906672412:109,246,433C/Guncertain significance
rs77041276812:109,246,444C/Tuncertain significance
rs128633404612:109,251,227A/Cuncertain significance
rs121453247012:109,251,230C/Auncertain significance
rs77402268012:109,251,279G/Clikely benign

Gene information from NCBI Gene. Variant classifications from ClinVar.